Document Detail


A variant or a "new" postaxial acrofacial dysostosis syndrome.
MedLine Citation:
PMID:  18286304     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
In this paper, we report a boy with remarkable phenotype and noteworthy radiographic abnormalities. He presented with distinctive facies, mesomelic shortening and asymmetry of the extremities, symmetrical ulnar and fibular ray absence in the hands and feet, with unique hypoplastic/dysplastic radiographic abnormalities. His mental development was normal. We believe that he represents a previously unreported form of the postaxial acrofacial dysostosis syndrome.
Authors:
Jerzy Sułko; Dariusz Kotulski; Kazimierz Kozlowski
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2008-02-20
Journal Detail:
Title:  European journal of pediatrics     Volume:  167     ISSN:  1432-1076     ISO Abbreviation:  Eur. J. Pediatr.     Publication Date:  2008 Dec 
Date Detail:
Created Date:  2008-10-20     Completed Date:  2009-02-05     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7603873     Medline TA:  Eur J Pediatr     Country:  Germany    
Other Details:
Languages:  eng     Pagination:  1385-8     Citation Subset:  IM    
Affiliation:
Orthopaedic and Traumatology Division, Children's University Hospital, Krakow, Poland.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / radiography*
Adolescent
Craniofacial Dysostosis / radiography*
Ear, External / abnormalities
Humans
Limb Deformities, Congenital / radiography*
Male
Mandibulofacial Dysostosis / radiography
Micrognathism / radiography
Phenotype
Syndrome

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