Document Detail


An unusual cause of posterior fossa mass: Lhermitte-Duclos disease.
MedLine Citation:
PMID:  20060133     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Lhermitte-Duclos disease (LDD) (dysplastic cerebellar gangliocytoma) is a rare disorder of unknown pathogenesis, presenting with signs and symptoms resulting from obstruction of cerebrospinal fluid flow and mass effect in the posterior fossa. Magnetic resonance imaging is the diagnostic modality of choice allowing preoperative diagnosis with characteristic findings. Surgery is the choice of treatment. The typical histopathological findings of LDD are characterized by widening of the molecular layer, absence of the Purkinje cell layer and hypertrophy in the granule cell layer. Herein we report an adolescent girl with LDD diagnosed preoperatively by the conventional and advanced MR techniques.
Authors:
Beg?l Ya?ci-K?peli; Kader K Oguz; M Asim Bilen; Bilgehan Yal?in; Nejat Akalan; M?nevver B?y?kpamuk?u
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2010-01-08
Journal Detail:
Title:  Journal of the neurological sciences     Volume:  290     ISSN:  1878-5883     ISO Abbreviation:  J. Neurol. Sci.     Publication Date:  2010 Mar 
Date Detail:
Created Date:  2010-02-01     Completed Date:  2010-05-13     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0375403     Medline TA:  J Neurol Sci     Country:  Netherlands    
Other Details:
Languages:  eng     Pagination:  138-41     Citation Subset:  IM    
Affiliation:
Department of Pediatric Oncology, Hacettepe University Institute of Oncology, 06100 Ankara, Turkey. drbegul@yahoo.com
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Cerebellar Neoplasms / pathology*,  physiopathology,  radiography
Cerebellum / pathology*,  physiopathology,  radiography
Cranial Fossa, Posterior / pathology*,  physiopathology
Female
Fourth Ventricle / pathology,  physiopathology,  radiography
Hamartoma Syndrome, Multiple / pathology*,  physiopathology,  radiography
Headache / etiology
Humans
Hydrocephalus / pathology,  physiopathology,  radiography
Intracranial Hypertension / etiology,  pathology,  physiopathology
Magnetic Resonance Imaging
Magnetic Resonance Spectroscopy
Neurosurgical Procedures
Tomography, X-Ray Computed
Treatment Outcome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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