| An unusual case of Budd-Chiari syndrome--a case report. | |
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MedLine Citation:
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PMID: 2964800 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The authors report a rare case of congenital Budd-Chiari syndrome in a twenty-eight-year-old male mongoloid. The patient was submitted to azygous-portal disconnection, because of the syndrome of portal hypertension supposedly due to cirrhosis of the liver. He died of hemorrhage of the liver on the third postoperative day. Autopsy revealed a congenital fibrotic obstruction of all suprahepatic veins, with a wide, round ligament containing a functional umbilical vein, which had been routinely ligated during surgery. An extensive review of the literature showed no similar report. The authors speculate that the inadvertent interruption of the round ligament, which until then had served as a pathway for venous draining of the liver, followed by ligation of the anastomoses between the portal and azygous systems, was the factor that triggered the lethal outcome. Thus, this appears to be the first case of congenital Budd-Chiari syndrome predominantly maintained at the expense of the round ligament of the liver, with a patent vascular branch. |
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Authors:
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R Corrêa de Araujo; R B Bestetti; J S Oliveira |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Angiology Volume: 39 ISSN: 0003-3197 ISO Abbreviation: Angiology Publication Date: 1988 Feb |
Date Detail:
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Created Date: 1988-04-18 Completed Date: 1988-04-18 Revised Date: 2007-11-15 |
Medline Journal Info:
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Nlm Unique ID: 0203706 Medline TA: Angiology Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 193-8 Citation Subset: IM |
Affiliation:
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Department of Pathology, Faculty of Medicine of Triângulo Mineiro, Uberaba, Brazil. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adult Budd-Chiari Syndrome / complications, congenital*, pathology Down Syndrome / complications Humans Liver / pathology Male Vena Cava, Inferior / pathology |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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