Document Detail


A syndrome of dislocated hips and radial heads, carpal coalition, and short stature in Puerto Rican children.
MedLine Citation:
PMID:  8423186     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
An orthopaedic syndrome that apparently had not been reported previously was identified in twenty-three children. Characteristics shared by all twenty-three children included Hispanic descent, residence in Puerto Rico, bilateral dislocation of the hip, dislocated radial heads, short stature, and other osseous anomalies. Twelve dislocated hips in six patients were not treated. All of these hips were functioning satisfactorily at the time of the review, but only four of the children had reached skeletal maturity. Sixteen hips in eight patients remained reduced after closed reduction. Of these eight patients, the four who were skeletally immature at the time of the review had a satisfactory result, and the four who were skeletally mature had an unsatisfactory result because of discomfort or fibrous ankylosis. Eighteen hips in nine patients were treated with a reduction augmented by some form of operation. All of these hips redislocated. Of the forty-six elbows in the twenty-three children, thirty-three were dislocated, as seen clinically and radiographically; eight were normal, both clinically and radiographically; and there was dysplasia at the radiocapitellar articulation of the remaining five. Twenty of the twenty-three children were found to have carpal coalitions. Fourteen children had scoliosis, and five of them were managed with spinal arthrodesis and correction. Three patients had an anomaly of the cervical spine, with one deformity causing symptoms and signs that were treated with decompression. Eight patients had talipes cavus bilaterally, which was not treated.
Authors:
H H Steel; R W Piston; M Clancy; R R Betz
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  The Journal of bone and joint surgery. American volume     Volume:  75     ISSN:  0021-9355     ISO Abbreviation:  J Bone Joint Surg Am     Publication Date:  1993 Feb 
Date Detail:
Created Date:  1993-02-25     Completed Date:  1993-02-25     Revised Date:  2010-10-25    
Medline Journal Info:
Nlm Unique ID:  0014030     Medline TA:  J Bone Joint Surg Am     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  259-64     Citation Subset:  AIM; IM    
Affiliation:
Shriners Hospitals for Crippled Children, Philadelphia Unit, Pennsylvania.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple / radiography
Body Height*
Carpal Bones / abnormalities*,  radiography
Child
Dislocations / congenital,  radiography*
Female
Hand / physiology
Hip Dislocation / radiography*
Humans
Male
Puerto Rico / ethnology
Radius / radiography*
Range of Motion, Articular
Scoliosis
Syndrome
United States
Wrist / physiology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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