Document Detail


On some cardiological aspects of Steinert's disease (myotonic dystrophy).
MedLine Citation:
PMID:  543205     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The authors investigated 10 ambulant patients with myotonic dystrophy, under 40 years of age (mean 22.3 years) and free of subjective heart complaints. Not only Ecg alterations but also kinetocardiographic changes and anomalies of the systolic intervals were rarer and milder than those found in patients with other neuromyopathies, namely Friedreich's disease and Duchenne's disease. This observation suggests that, at least in older patients, not all the cardiac alterations usually attributed to myotonic dystrophy are really imputable to the disease. On the other hand, the observed echocardiographic alterations (reduction of per cent systolic-diastolic variation of internal diameter of the left ventricle and/or the ejection fraction) apparently indicate an early tendency to modification of left ventricular function in patients with myotonic dystrophy. Since other authors have found cardiac anomalies in this disease before the onset of any neurological manifestations, the possibility emerges that some cases of myocardial disease interpreted as "primitive" might in reality be secondary to undetected myopathy.
Authors:
G Beulcke; F Casazza; B Colombo; M Morpurgo; G Scannavini
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Zeitschrift für Kardiologie     Volume:  68     ISSN:  0300-5860     ISO Abbreviation:  Z Kardiol     Publication Date:  1979 Dec 
Date Detail:
Created Date:  1980-06-25     Completed Date:  1980-06-25     Revised Date:  2007-11-15    
Medline Journal Info:
Nlm Unique ID:  0360430     Medline TA:  Z Kardiol     Country:  GERMANY, WEST    
Other Details:
Languages:  eng     Pagination:  848-54     Citation Subset:  IM    
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Aorta / pathology
Arrhythmias, Cardiac / etiology*
Child
Female
Heart / physiopathology
Heart Septum / pathology
Heart Ventricles / pathology
Humans
Male
Myotonic Dystrophy / complications*

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