Document Detail


The role of sexual related Y gene detection in the diagnosis of patients with gonadal dysgenesis.
MedLine Citation:
PMID:  11780190     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: To clarify the role of sexual related Y (SRY) gene detection in the diagnosis of gonadal dysgenesis. METHODS: Sixteen cases of gonadal dysgenesis were included in this study: 5 with androgen insensitivity syndrome, 1 with 17-alpha-hydroxylase deficiency, 4 with true hermaphrodite, 2 with 45, X/46, XY gonadal dysgenesis, 1 with 45, X gonadal dysgenesis, 1 with XY pure gonadal dysgenesis, 1 with testicular regression, and 1 XY female who gave birth to a normal baby. SRY gene was detected by using polymerase chain reaction (PCR) in blood and gonad samples and by direct sequencing of the SRY motif. RESULTS: Among the 16 cases, 15 were blood SRY positive, among which 13 (86.7%) showed the presence of testicular tissue, and 2 showed ovaries without testicular tissue. One SRY negative case showed the presence of testicular tissue. In 3 cases, SRY detection in gonadal tissue correlated with pathological findings but not with blood karyotype. The correlation between peripheral blood SRY and the pathology of the gonads was 81.25% and the correlation between the presence of peripheral blood Y chromosome and pathology of the gonads was 68.75%. Sequencing of the SRY motif in an XY female who gave birth to a normal baby showed no mutation. CONCLUSIONS: SRY detection is more sensitive and specific than blood karyotype in the prediction of the presence of testicular tissue. Peripheral blood karyotype does not necessarily reflect gonadal type. There may be testicular related factors other than the SRY gene.
Authors:
Q Yu; S Huang; L Ye; L Feng; F He; J Ye; C Gu; Q Ge
Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Chinese medical journal     Volume:  114     ISSN:  0366-6999     ISO Abbreviation:  Chin. Med. J.     Publication Date:  2001 Feb 
Date Detail:
Created Date:  2002-01-08     Completed Date:  2002-02-13     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  7513795     Medline TA:  Chin Med J (Engl)     Country:  China    
Other Details:
Languages:  eng     Pagination:  128-31     Citation Subset:  IM    
Affiliation:
Department of Obstetrics and Gynecology, Peking Union Medical College Hospital, CAMS, Beijing 100730, China.
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MeSH Terms
Descriptor/Qualifier:
DNA / genetics
DNA-Binding Proteins / genetics*
Female
Gonadal Dysgenesis / diagnosis*,  genetics
Humans
Karyotyping
Male
Nuclear Proteins*
Polymerase Chain Reaction
Sex-Determining Region Y Protein
Transcription Factors*
Chemical
Reg. No./Substance:
0/DNA-Binding Proteins; 0/Nuclear Proteins; 0/SRY protein, human; 0/Sex-Determining Region Y Protein; 0/Transcription Factors; 9007-49-2/DNA

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