Document Detail


The role of lymphoscintigraphy in the diagnosis of lymphedema in Turner syndrome.
MedLine Citation:
PMID:  19927901     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Lymphedema can be present in patients affected by Turner syndrome (TS) with the dorsum of the hands and feet most commonly affected. This lymphedema results from underdevelopment of the lymphatic system before birth, and it usually decreases during childhood. The aim of our study was to evaluate the role of lymphoscintigraphy as a diagnostic tool in patients with TS to assess possible impairments in the lymphatic system. Eighteen patients with TS were karyotyped to confirm diagnosis and were evaluated by lymphoscintigraphy. Lymphatic dysfunction was demonstrated in 15/18 patients. Lymphoscintigraphic studies showed: 1) lymphatic channels, 2) collateral lymphatic channels, 3) interrupted lymphatic structures, and 4) lymph nodes of the deep lymphatic system. Our data demonstrate that lymphoscintigraphy should be mandatory not only in patients affected by Turner syndrome with signs of lymphatic dysplasia but also in those with minimal or absent signs of lymphatic impairment in order to obtain a very early diagnosis and to provide substantial information for possible medical or surgical treatment.
Authors:
C Bellini; E Di Battista; F Boccardo; C Campisi; G Villa; G Taddei; C Traggiai; A Amisano; A Amisamo; P Polo Perucchin; C S Benfenati; E Bonioli; R Lorini
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Lymphology     Volume:  42     ISSN:  0024-7766     ISO Abbreviation:  Lymphology     Publication Date:  2009 Sep 
Date Detail:
Created Date:  2009-11-20     Completed Date:  2009-12-23     Revised Date:  2010-03-11    
Medline Journal Info:
Nlm Unique ID:  0155112     Medline TA:  Lymphology     Country:  United States    
Other Details:
Languages:  eng     Pagination:  123-9     Citation Subset:  IM    
Affiliation:
Neuromuscular Diseases Unit, Department of Pediatrics, University of Genoa, Genoa, Italy. carlobellini@ospedale-gaslini.ge.it
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Adult
Child
Child, Preschool
Female
Humans
Lymphedema / radionuclide imaging*
Male
Radiopharmaceuticals / diagnostic use
Technetium Tc 99m Aggregated Albumin / diagnostic use
Turner Syndrome / radionuclide imaging*
Chemical
Reg. No./Substance:
0/Radiopharmaceuticals; 0/Technetium Tc 99m Aggregated Albumin; 0/technetium Tc 99m nanocolloid
Comments/Corrections
Erratum In:
Lymphology. 2009 Dec;42(4):202
Note: Amisamo, A [corrected to Amisano, A]

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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