Document Detail


A rare case of internal jugular vein aneurysmal degeneration in a type 1 neurofibromatosis complicated by potentially life-threatening thrombosis.
MedLine Citation:
PMID:  21684713     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Type 1 neurofibromatosis (NF1) is an autosomal dominant disorder characterized by multiple forms of neural crest cell proliferation. Associated venous malformations are extremely rare. We present a case of a giant thrombosed internal jugular aneurysm with brachiocephalic vein thrombosis in an NF1 patient. Surgical correction required prophylactic left brachiocephalic vein ligation, aneurysm evacuation, and proximal jugular vein ligation. Extreme vein friability caused severe intraoperative bleeding. Vein wall histology confirmed neurofibromatosis infiltration. Jugular vein aneurysm and infiltration in NF1, although exceedingly rare, can pose a serious threat to the patient during surgical correction, with major vessel thrombosis enhancing morbidity and mortality.
Authors:
Mirko Belcastro; Andrea Palleschi; Riccardo A Trovato; Ruggero Landini; Maurizio Di Bisceglie; Armando Natale
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of vascular surgery     Volume:  54     ISSN:  1097-6809     ISO Abbreviation:  J. Vasc. Surg.     Publication Date:  2011 Oct 
Date Detail:
Created Date:  2011-10-05     Completed Date:  2011-11-18     Revised Date:  2012-10-03    
Medline Journal Info:
Nlm Unique ID:  8407742     Medline TA:  J Vasc Surg     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1170-3     Citation Subset:  IM    
Copyright Information:
Copyright © 2011 Society for Vascular Surgery. Published by Mosby, Inc. All rights reserved.
Affiliation:
Vascular Surgery Unit, Misericordia Hospital, Grosseto, Italy. mirkoblc@fastwebnet.it
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MeSH Terms
Descriptor/Qualifier:
Aneurysm, Ruptured / diagnosis,  etiology*,  surgery
Female
Humans
Jugular Veins* / pathology,  radiography,  surgery
Ligation
Middle Aged
Neurofibromatosis 1 / complications*,  diagnosis
Tomography, X-Ray Computed
Treatment Outcome
Vascular Surgical Procedures
Venous Thrombosis / diagnosis,  etiology*,  surgery

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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