Document Detail

A primary extraosseous Ewing sarcoma in the cerebellopontine angle of a child: review of relevant literature and case report.
MedLine Citation:
PMID:  21107154     Owner:  NLM     Status:  MEDLINE    
BACKGROUND AND IMPORTANCE: We report the occurrence of a primary intracranial extraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumor (EES/pPNET) in the cerebellopontine angle in a child.
CLINICAL PRESENTATION: A 10-year-old girl presented with symptoms and signs of an infratentorial space-occupying lesion that was confirmed by magnetic resonance imaging and followed up by subtotal surgical resection. Tumor cells displayed membranous expression of CD99, and one of the typical translocations of EES/pPNET (chromosome 22) was demonstrated by cytogenetic analysis.
CONCLUSION: The literature regarding the histopathological, molecular, radiological, prognostic, and therapeutic features of intracranial EES/pPNET is reviewed, emphasizing the distinction of this entity from the central PNET. Although exceptionally rare, intracranial EES/pPNET should be considered in the differential diagnosis of lesions in the cerebellopontine angle.
E J dos Santos Rubio; B S Harhangi; J M Kros; A J P E Vincent; C M F Dirven
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Neurosurgery     Volume:  67     ISSN:  1524-4040     ISO Abbreviation:  Neurosurgery     Publication Date:  2010 Dec 
Date Detail:
Created Date:  2010-11-25     Completed Date:  2011-03-22     Revised Date:  2011-08-25    
Medline Journal Info:
Nlm Unique ID:  7802914     Medline TA:  Neurosurgery     Country:  United States    
Other Details:
Languages:  eng     Pagination:  E1852-6     Citation Subset:  IM    
Department of Neurosurgery, Erasmus Medical Center, Rotterdam, the Netherlands.
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MeSH Terms
Bone Neoplasms / complications*,  pathology
Cerebellar Neoplasms / complications*,  pathology
Cerebellopontine Angle / pathology*
Magnetic Resonance Imaging
Sarcoma, Ewing's / complications*,  pathology

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