Document Detail


The pathology of the heart conduction system in congenital heart block.
MedLine Citation:
PMID:  17029919     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The incidence of congenital complete heart block is estimated in 1 of 2500-20,000 births. Many cases are isolated (found in an otherwise normal heart) and the pathology of the heart conduction system is variable. We report a 51-year-old man with the diagnosis of complete heart block, with a permanent pacemaker. No family history of rhythm disturbances was available. The patient presented and endocarditis after replacement of the pacemaker battery. The prognosis was poor and the patient died three months later. Autopsy examination showed signs of shock, of septic origin. The heart was hypertrophic (450g) and the left ventricle thickened. Histopathological examination of the heart conduction system showed that the sinus and atrioventricular nodes were normal, but the His bundle was interrupted and replaced by fibrous tissue. No inflammatory signs were present. Loss of conducting fibres and their replacement by fibrous tissue is the most common pathological process in complete heart block. In this case His bundle was mostly affected, different to Lev's disease where the process is more distal (branching atrioventricular bundle) and to Lenegre's disease, which shows a diffuse damage in the conducting system.
Authors:
J M Suárez-Peñaranda; J I Muñoz; M S Rodríguez-Calvo; J A Ortíz-Rey; L Concheiro
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2006-10-06
Journal Detail:
Title:  Journal of clinical forensic medicine     Volume:  13     ISSN:  1353-1131     ISO Abbreviation:  J Clin Forensic Med     Publication Date:    2006 Aug-Nov
Date Detail:
Created Date:  2006-10-23     Completed Date:  2007-02-08     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9434927     Medline TA:  J Clin Forensic Med     Country:  Scotland    
Other Details:
Languages:  eng     Pagination:  341-3     Citation Subset:  IM    
Affiliation:
Department of Pathology and Forensic Sciences, University of Santiago de Compostela, Hospital Clínico, Travesía de Choupana s/n, 15702 Santiago de Compostela, Spain. jsuarezp@usc.es
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MeSH Terms
Descriptor/Qualifier:
Autopsy
Bundle of His / pathology*
Diagnosis, Differential
Forensic Medicine
Heart Block / congenital,  pathology*
Heart Conduction System / pathology
Humans
Male
Middle Aged

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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