Document Detail


p53 promotes cardiac dysfunction in diabetic mellitus caused by excessive mitochondrial respiration-mediated reactive oxygen species generation and lipid accumulation.
MedLine Citation:
PMID:  22075967     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
BACKGROUND: Diabetic cardiomyopathy is characterized by energetic dysregulation caused by glucotoxicity, lipotoxicity, and mitochondrial alterations. p53 and its downstream mitochondrial assembly protein, synthesis of cytochrome c oxidase 2 (SCO2), are important regulators of mitochondrial respiration, whereas the involvement in diabetic cardiomyopathy remains to be determined.
METHODS AND RESULTS: The role of p53 and SCO2 in energy metabolism was examined in both type I (streptozotocin [STZ] administration) and type II diabetic (db/db) mice. Cardiac expressions of p53 and SCO2 in 4-week STZ diabetic mice were upregulated (185% and 152% versus controls, respectively, P<0.01), with a marked decrease in cardiac performance. Mitochondrial oxygen consumption was increased (136% versus control, P<0.01) in parallel with augmentation of mitochondrial cytochrome c oxidase (complex IV) activity. Reactive oxygen species (ROS)-damaged myocytes and lipid accumulation were increased in association with membrane-localization of fatty acid translocase protein FAT/CD36. Antioxidant tempol reduced the increased expressions of p53 and SCO2 in STZ-diabetic hearts and normalized alterations in mitochondrial oxygen consumption, lipid accumulation, and cardiac dysfunction. Similar results were observed in db/db mice, whereas in p53-deficient or SCO2-deficient diabetic mice, the cardiac and metabolic abnormalities were prevented. Overexpression of SCO2 in cardiac myocytes increased mitochondrial ROS and fatty acid accumulation, whereas knockdown of SCO2 ameliorated them.
CONCLUSIONS: Myocardial p53/SCO2 signal is activated by diabetes-mediated ROS generation to increase mitochondrial oxygen consumption, resulting in excessive generation of mitochondria-derived ROS and lipid accumulation in association with cardiac dysfunction.
Authors:
Hideo Nakamura; Satoaki Matoba; Eri Iwai-Kanai; Masaki Kimata; Atsushi Hoshino; Mikihiko Nakaoka; Maki Katamura; Yoshifumi Okawa; Makoto Ariyoshi; Yuichiro Mita; Koji Ikeda; Mitsuhiko Okigaki; Souichi Adachi; Hideo Tanaka; Tetsuro Takamatsu; Hiroaki Matsubara
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Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't     Date:  2011-11-09
Journal Detail:
Title:  Circulation. Heart failure     Volume:  5     ISSN:  1941-3297     ISO Abbreviation:  Circ Heart Fail     Publication Date:  2012 Jan 
Date Detail:
Created Date:  2012-01-18     Completed Date:  2012-04-13     Revised Date:  2012-05-24    
Medline Journal Info:
Nlm Unique ID:  101479941     Medline TA:  Circ Heart Fail     Country:  United States    
Other Details:
Languages:  eng     Pagination:  106-15     Citation Subset:  IM    
Affiliation:
Department of Cardiovascular Medicine, Kyoto Prefectural University School of Medicine, Kawaramachi-Hirokoji, Kamigyo-ku, Kyoto, Japan.
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MeSH Terms
Descriptor/Qualifier:
Animals
Antigens, CD36 / metabolism
Diabetes Complications / complications*,  metabolism
Diabetes Mellitus, Experimental / chemically induced,  complications*,  metabolism
Diabetic Cardiomyopathies / etiology*,  metabolism
Disease Models, Animal
Electron Transport Complex IV / genetics,  metabolism
Fatty Acids / metabolism
Lipid Metabolism / physiology*
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Mice, Mutant Strains
Mitochondria, Heart / metabolism*
Myocytes, Cardiac / metabolism
Oxygen Consumption / physiology
Reactive Oxygen Species / metabolism*
Streptozocin / adverse effects
Tumor Suppressor Protein p53 / deficiency,  genetics,  metabolism*
Chemical
Reg. No./Substance:
0/Antigens, CD36; 0/Fatty Acids; 0/Reactive Oxygen Species; 0/Tumor Suppressor Protein p53; 18883-66-4/Streptozocin; EC 1.9.3.-/SCO2 protein, mouse; EC 1.9.3.1/Electron Transport Complex IV

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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