| A new neurocutaneous syndrome possibly related to Ota's nevus. | |
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MedLine Citation:
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PMID: 8229056 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The case of a 42-year-old Sudanese man is reported who had developed hyperpigmentation of the left face and rapidly progressive right hemiparesis followed by myoclonus at the age of 30. Blue-grey hyperpigmentation was noted in the territory of the left ophthalmic, maxillary and mandibular trigeminal nerve branches, with alopecia of the right face and axilla. CT of the brain revealed left-sided paraventricular calcifications and MRI showed atrophy of the left cerebral hemisphere and mesencephalon, a calcified haemangioma in the left basal ganglia, an old infarct in the right central pons, and cerebellar atrophy. This case resembles Ota's syndrome; however, atypical distribution of the facial nevus, the epidermal location of hyperpigmentation, and the combination of vascular and degenerative cerebral malformations indicate that this is a new hitherto unreported neurocutaneous vascular syndrome. |
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Authors:
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S M al Deeb; Y Bahou |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Journal of the neurological sciences Volume: 118 ISSN: 0022-510X ISO Abbreviation: J. Neurol. Sci. Publication Date: 1993 Aug |
Date Detail:
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Created Date: 1993-12-03 Completed Date: 1993-12-03 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0375403 Medline TA: J Neurol Sci Country: NETHERLANDS |
Other Details:
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Languages: eng Pagination: 92-6 Citation Subset: IM |
Affiliation:
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Department of Clinical Neurosciences, Riyadh Armed Forces Hospital, Saudi Arabia. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Adult Atrophy Brain / pathology, radionuclide imaging Electroencephalography Humans Hyperpigmentation / pathology* Magnetic Resonance Imaging Male Nervous System Diseases / pathology*, physiopathology, radiography Nevus of Ota / pathology*, physiopathology, radiography Syndrome Tomography, X-Ray Computed |
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