| A malignant peripheral nerve sheath tumor of the mediastinum in a patient with neurofibromatosis type 1: report of a case. | |
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MedLine Citation:
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PMID: 18820872 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Malignant peripheral nerve sheath tumor (MPNST) is rare, but its association with neurofibromatosis type 1 (NF1) is well known. A 56-year-old man with NF1 was referred to our hospital for investigation of dyspnea. Computed tomography showed a huge mass occupying the right thorax and invading the inferior vena cava. A salvage resection was performed to alleviate the developing hypoxemia. Histological examination confirmed an MPNST. The tumor regrew rapidly and the patient died 6 weeks after the resection. This case report reinforces the importance of monitoring patients with NF1 carefully because of their increased risk of the development of malignant neoplasms. |
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Authors:
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Riken Kawachi; Hidefumi Takei; Goh Furuyashiki; Yoshihiko Koshi-Ishi; Tomoyuki Goya |
Publication Detail:
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Type: Case Reports; Journal Article Date: 2008-09-27 |
Journal Detail:
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Title: Surgery today Volume: 38 ISSN: 0941-1291 ISO Abbreviation: Surg. Today Publication Date: 2008 |
Date Detail:
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Created Date: 2008-09-29 Completed Date: 2009-03-31 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9204360 Medline TA: Surg Today Country: Japan |
Other Details:
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Languages: eng Pagination: 945-7 Citation Subset: IM |
Affiliation:
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Department of Surgery, Kyorin University School of Medicine, 6-20-2 Shinkawa, Mitaka, Tokyo, 181-8611, Japan. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Fatal Outcome Humans Male Mediastinal Neoplasms / complications*, radiography, surgery* Middle Aged Nerve Sheath Neoplasms / complications*, radiography, surgery* Neurofibromatosis 1 / complications* Tomography, X-Ray Computed |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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