Document Detail


Is the lattice dystrophy of the cornea due to developmental anomalies of neural crest cells during embryogenesis (neurocristopathies)?
MedLine Citation:
PMID:  18333410     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
With the present paper authors try to give an embryological approach in understanding etiopathogenesis of lattice corneal dystrophy (LCD). The case of a 41-years-old man affected by isolated LCD has been examined at the Ophtalmologic Clinic of the University of Catania, Italy. Sore cornea has been excised during cornea transplantation, and it has been examined by transmission electron microscopy (TEM). Results confirm classic submicroscopic findings described in literature. However these findings offer possibility to consider an embryological interpretation of LCD pathogenesis. Our findings with those of literature put forward hypothesis of a hereditary etiopathogenetical role exerted by keratocytes, direct derivatives of neural crest cells during embryogenesis, probably via an abnormal gene expression in producing proteinaceous precursor of amyloid substance (APP). LCD could be considered a neurocristopathy.
Authors:
Paola Castrogiovanni; Rosa Imbesi; Fabio D'Amico; Vera Mazzone; Nicolò Cavallaro
Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Italian journal of anatomy and embryology = Archivio italiano di anatomia ed embriologia     Volume:  112     ISSN:  1122-6714     ISO Abbreviation:  Ital J Anat Embryol     Publication Date:    2007 Oct-Dec
Date Detail:
Created Date:  2008-03-12     Completed Date:  2008-04-25     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9612303     Medline TA:  Ital J Anat Embryol     Country:  Italy    
Other Details:
Languages:  eng     Pagination:  255-66     Citation Subset:  IM    
Affiliation:
Department of Biomedical Science, University of Catania, Italy. pacastro@unict.it
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MeSH Terms
Descriptor/Qualifier:
Adult
Amyloid beta-Protein / biosynthesis
Amyloid beta-Protein Precursor / genetics,  metabolism
Cornea / abnormalities*,  pathology*,  physiopathology
Corneal Dystrophies, Hereditary / genetics,  pathology*,  physiopathology
Descemet Membrane / metabolism,  pathology
Embryonic Development / physiology
Endothelium, Corneal / metabolism,  pathology
Genetic Predisposition to Disease / genetics
Humans
Keratinocytes / metabolism,  pathology
Male
Microscopy, Electron, Transmission
Neural Crest / cytology*,  metabolism
Chemical
Reg. No./Substance:
0/Amyloid beta-Protein; 0/Amyloid beta-Protein Precursor

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