Document Detail


The history of progressive muscular atrophy: syndrome or disease?
MedLine Citation:
PMID:  18299524     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Since its first description more than a century ago, there has been much debate about the diagnostic entity progressive muscular atrophy (PMA). Initially, PMA included all forms of progressive amyotrophy. With the identification of several myogenic and neurogenic diseases and the recognition of amyotrophic lateral sclerosis (ALS), PMA was deemed to disappear as a nosologic entity at the end of the 19th century. In the last century, various other lower motor neuron syndromes were distinguished which may previously have been designated as cases of PMA. In contrast, several observations provided evidence that PMA can be linked both clinically and pathologically to ALS. Therefore, PMA should be considered as a syndromal subtype within a clinical spectrum of motor neuron diseases.
Authors:
Jeldican Visser; J M B Vianney de Jong; Marianne de Visser
Related Documents :
12968834 - Charles bonnet syndrome: visual hallucination and multiple sclerosis.
16681064 - A traumatic bitemporal hemianopia with macular sparing.
21204804 - Stxbp1 mutations cause not only ohtahara syndrome but also west syndrome--result of jap...
3566024 - Pseudo-achondroplastic variant of multiple epiphyseal dysplasia with cataract and vitil...
12664274 - A case of autism in a child with apert's syndrome.
18063214 - Tracheal anomalies complicating ventilation of an infant with apert syndrome.
Publication Detail:
Type:  Historical Article; Journal Article    
Journal Detail:
Title:  Neurology     Volume:  70     ISSN:  1526-632X     ISO Abbreviation:  Neurology     Publication Date:  2008 Feb 
Date Detail:
Created Date:  2008-02-26     Completed Date:  2008-03-07     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  0401060     Medline TA:  Neurology     Country:  United States    
Other Details:
Languages:  eng     Pagination:  723-7     Citation Subset:  AIM; IM    
Affiliation:
Department of Neurology, Academic Medical Center, Amsterdam, The Netherlands. j.visser@amc.uva.nl
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
History, 19th Century
History, 20th Century
History, 21st Century
Humans
Motor Neuron Disease / history*
Muscular Atrophy / history*
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Evaluation of the assessment and grading of medical students on a neurology clerkship.
Next Document:  Diagnosis and treatment of dementia: 1. Risk assessment and primary prevention of Alzheimer disease.