Document Detail


The H syndrome.
MedLine Citation:
PMID:  20199414     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The H syndrome is a recently defined autosomal recessive genodermatosis caused by mutations in the nucleoside transporter hENT3. It is characterized by cutaneous changes of progressive sclerosis, hyperpigmentation, and hypertrichosis that follow a specific pattern and are associated with multiple systemic manifestations. A case is presented and a brief review is introduced based on the few related reports.
Authors:
Ekramy A El-Khateeb
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Pediatric dermatology     Volume:  27     ISSN:  1525-1470     ISO Abbreviation:  Pediatr Dermatol     Publication Date:    2010 Jan-Feb
Date Detail:
Created Date:  2010-03-04     Completed Date:  2010-06-02     Revised Date:  2011-01-11    
Medline Journal Info:
Nlm Unique ID:  8406799     Medline TA:  Pediatr Dermatol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  65-8     Citation Subset:  IM    
Affiliation:
Department of Dermatology, Venereology and Andrology, Ain Shams University, Cairo, Egypt. krmhmd@yahoo.com
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MeSH Terms
Descriptor/Qualifier:
Bone Diseases / genetics*,  radiography
Female
Humans
Hyperpigmentation / genetics*,  pathology
Hypertrichosis / genetics*,  pathology
Nucleoside Transport Proteins / genetics*
Skin Diseases, Genetic / genetics*,  pathology
Young Adult
Chemical
Reg. No./Substance:
0/Nucleoside Transport Proteins; 0/SLC29A3 protein, human

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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