Document Detail


The fifteen years of discoveries that shaped molecular electrophysiology: time for appraisal.
MedLine Citation:
PMID:  20724724     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
This article serves as an introductory overview to a thematic review series that will present the latest advancements in the field of inherited arrhythmias. This area of cardiac electrophysiology started approximately 15 years ago thanks to the contribution of Mark Keating and coworkers, who discovered the molecular basis of long QT syndrome. The field rapidly expanded when clinicians, molecular biologists, geneticists, and cellular electrophysiologists, who undertook an impressive collaborative effort to clarify the genetic basis of "cardiac channelopathies." As a result of this hard work, the paradigms for diagnosis and management of patients with inherited arrhythmogenic diseases were substantially modified, demonstrating once more the value of "translational research." As more and more genes have been implicated in the genesis of inherited arrhythmias, we keep broadening our understanding of the complexity of ion channels and their multifaceted regulatory processes. Despite the fact that several discoveries have already been made, the field is facing new challenges that are attracting young investigators who share with the pioneers the ambitious goal of finding new therapies and even a cure for these conditions.
Authors:
Silvia G Priori
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Publication Detail:
Type:  Journal Article; Research Support, Non-U.S. Gov't; Review    
Journal Detail:
Title:  Circulation research     Volume:  107     ISSN:  1524-4571     ISO Abbreviation:  Circ. Res.     Publication Date:  2010 Aug 
Date Detail:
Created Date:  2010-08-20     Completed Date:  2010-09-16     Revised Date:  2011-11-24    
Medline Journal Info:
Nlm Unique ID:  0047103     Medline TA:  Circ Res     Country:  United States    
Other Details:
Languages:  eng     Pagination:  451-6     Citation Subset:  IM    
Affiliation:
Division of Cardiology and Molecular Cardiology, Fondazione Salvatore Maugeri, Via S Maugeri 10/10 degrees, 27100 Pavia, Italy. silvia.priori@nyumc.org
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MeSH Terms
Descriptor/Qualifier:
Animals
Arrhythmias, Cardiac / genetics,  physiopathology
Electrophysiological Phenomena / genetics*,  physiology
Genetic Testing / methods*,  trends*
Humans
Long QT Syndrome / genetics*,  physiopathology*
Mutation / genetics
Grant Support
ID/Acronym/Agency:
GGP06007//Telethon

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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