| The duplicated longitudinal epiphysis or "kissing delta phalanx": evolution and variation in three different disorders. | |
| | |
MedLine Citation:
|
PMID: 15138725 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
|
BACKGROUND: The delta phalanx, also known as the delta bone, or longitudinal epiphyseal bracket (LEB), has been described in a variety of syndromes and dysplasias. However, the "kissing delta phalanx" is not as well recognized in the literature; it consists of a duplicated longitudinal bracketed epiphysis, or a complex of two adjacent delta bones, with opposing convex portions facing each other. Magnetic resonance imaging of the kissing delta phalanx has not been previously described. OBJECTIVE: To describe the evolution, variation and associated osseous anomalies of the kissing delta phalanx in three patients with distinct distal limb malformations using both plain films and magnetic resonance imaging. RESULTS: Patient 1 had Rubinstein-Taybi syndrome and, in addition to a kissing delta phalanx in both feet, had corresponding delta metatarsals (MT1). Patient 2 had Cenani-Lenz syndactyly with distinct variation of the kissing delta phalanx in each hand. He had a disorganized appearance to the phalanges, metacarpal fusions and carpal coalitions. Patient 3 had an isolated oligosyndactyly of the left hand with metacarpal fusions and carpal coalitions. All three patients were followed over time. We describe two types of kissing delta phalanges: separated (without fusion of the corresponding epiphyseal brackets) and nonseparated (with fusion of the corresponding epiphyseal brackets). Both types can be seen in the same patient and are a reflection of the relative degree of segmentation of the two delta bones. CONCLUSION: The appearance of this rare osseous abnormality changes with time and can be found in a limited number of uncommon disorders. It can also be found in association with other osseous anomalies of the distal extremities; therefore magnetic resonance imaging early in life can greatly assist in surgical planning. Recognition of the kissing delta phalanx may be an important radiological clue to diagnosis of these rare disorders. |
| | |
Authors:
|
Alison M Elliott; Jane A Evans; Albert E Chudley; Martin H Reed |
Related Documents
:
|
15252095 - The efficacy of ultrasound in the evaluation of dynamic scapholunate ligamentous instab... 3574675 - Repeater f waves: a comparison of sensitivity with sensory antidromic wrist-to-palm lat... 11993525 - Conservative treatment options for carpal tunnel syndrome: a systematic review of rando... 22319315 - Relaxation time estimation from complex magnetic resonance images. 7062185 - The prognostic value of computed tomography of the brain in asphyxiated premature infants. 15204295 - The development of risk assessment models for carpal tunnel syndrome: a case-referent s... |
Publication Detail:
|
Type: Case Reports; Journal Article; Research Support, Non-U.S. Gov't Date: 2004-05-06 |
Journal Detail:
|
Title: Skeletal radiology Volume: 33 ISSN: 0364-2348 ISO Abbreviation: Skeletal Radiol. Publication Date: 2004 Jun |
Date Detail:
|
Created Date: 2004-05-17 Completed Date: 2004-11-02 Revised Date: 2006-11-15 |
Medline Journal Info:
|
Nlm Unique ID: 7701953 Medline TA: Skeletal Radiol Country: Germany |
Other Details:
|
Languages: eng Pagination: 345-51 Citation Subset: IM |
Copyright Information:
|
Copyright 2004 ISS |
Affiliation:
|
Department of Biochemistry and Medical Genetics, University of Manitoba, 770 Bannatyne Avenue, Winnipeg, Manitoba, R3E 0W3, Canada. amelliott@mts.net |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
Child, Preschool Epiphyses / abnormalities*, growth & development Female Fingers / abnormalities*, growth & development Humans Infant Male Rubinstein-Taybi Syndrome / pathology, radiography* Syndactyly / pathology, radiography* Syndrome Toes / abnormalities*, growth & development |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: MRI of hemangiopericytoma in the sacrum.
Next Document: Shoe rim and shoe buckle pseudotumor of the ankle in elite and professional figure skaters and snowb...