Document Detail

The congenital porto-caval fistula: a unique presentation and novel intervention.
MedLine Citation:
PMID:  18085682     Owner:  NLM     Status:  MEDLINE    
Congenital porto-caval fistulas are uncommon vascular malformations with a varied clinical presentation beginning in infancy and spanning late adulthood. We report a 14-year-old male who presented with dyspnea and cough. His past medical history was significant for a chronic non-immune hemolytic anemia, thrombocytopenia, coagulopathy and a learning disability. He was found to have severe pulmonary hypertension and hyperammonemia associated with a large congenital porto-caval fistula. The abnormal vessel was occluded via endovascular covered stent placement in the vena cava. His pulmonary hypertension has improved remarkably while his chronic anemia, thrombocytopenia and ammonia have normalized to allow improved cognitive performance.
Wynton Hoover; Veda Ackerman; Marcus Schamberger; Manjusha Kumar; Francis Marshalleck; Mark Hoyer
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric pulmonology     Volume:  43     ISSN:  1099-0496     ISO Abbreviation:  Pediatr. Pulmonol.     Publication Date:  2008 Feb 
Date Detail:
Created Date:  2008-01-02     Completed Date:  2008-03-18     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8510590     Medline TA:  Pediatr Pulmonol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  196-9     Citation Subset:  IM    
Copyright Information:
Copyright 2007 Wiley-Liss, Inc.
Division of Pediatric Pulmonology, Riley Hospital for Children, Indiana University, Indianapolis, Indiana, USA.
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MeSH Terms
Anemia / complications
Chronic Disease
Cough / etiology
Dyspnea / etiology
Hyperammonemia / complications,  etiology
Hypertension, Pulmonary / etiology*
Learning Disorders / etiology
Portal Vein* / radiography
Pulmonary Artery / pathology
Thrombocytopenia / complications
Tomography, X-Ray Computed
Treatment Outcome
Vascular Fistula / complications,  congenital*,  diagnosis*,  radiography,  therapy
Vena Cava, Inferior* / radiography

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