Document Detail


The clinical presentation and electrophysiological findings of porphyric neuropathies: a follow-up study.
MedLine Citation:
PMID:  24985076     Owner:  NLM     Status:  Publisher    
Abstract/OtherAbstract:
Introduction: A case series of acute intermittent porphyria (AIP) is described which focuses on the clinical course of the disease with regard to neurological manifestations of the peripheral nervous system. Methods: Eight patients were diagnosed with AIP on the basis of characteristic clinical findings, erythrocyte porphobilinogendeaminase activity, neuropathic patterns, serial changes in nerve conduction studies (NCS), and temporal relationship of central nervous system involvement. Results: Six patients diagnosed with AIP less than 2 months after symptom onset had neuropathy that was predominantly upper extremity, motor, and proximal. NCS recovery rates were slower in the lower than the upper limbs. Two patients diagnosed more than 2 months after symptom onset had distal sensorimotor polyneuropathy. Discussion: The findings of this case series suggest that the peripheral nerves may be differentially and selectively involved in different diagnostic stages of porphyric neuropathy. © 2014 Wiley Periodicals, Inc.
Authors:
Chi-Lin Wu; Long-Sun Ro; Shih-Ming Jung; Tzung-Chang Tsai; Chun-Che Chu; Rong-Kuo Lyu; Chin-Chang Huang; Hung-Chou Kuo
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Publication Detail:
Type:  JOURNAL ARTICLE     Date:  2014-7-2
Journal Detail:
Title:  Muscle & nerve     Volume:  -     ISSN:  1097-4598     ISO Abbreviation:  Muscle Nerve     Publication Date:  2014 Jul 
Date Detail:
Created Date:  2014-7-2     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7803146     Medline TA:  Muscle Nerve     Country:  -    
Other Details:
Languages:  ENG     Pagination:  -     Citation Subset:  -    
Copyright Information:
Copyright © 2014 Wiley Periodicals, Inc., a Wiley company.
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