| The clinical and laboratory manifestations of Iranian patients with cystic fibrosis. | |
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MedLine Citation:
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PMID: 20560247 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Cystic fibrosis (CF) is a hereditary disease, characterized by chronic pulmonary disease, pancreatic insufficiency and abnormal electrolytes in the sweat. In order to evaluate the clinical manifestations and laboratory findings of Iranian children with CF during a 10-year period, 243 CF patients, with a median age of 5 months, were investigated in this study. The most common manifestations were gastrointestinal disorders and respiratory manifestations. Cough was the most common symptom, followed by malnutrition, diarrhea, respiratory distress, and vomiting. The frequency of these findings after treatment was significantly decreased in comparison with the period before diagnosis. During the mean follow-up of 40.9 months, seven cases died due to severe infections. Cystic fibrosis as a common genetic disorder should be considered in any child with recurrent gastrointestinal and respiratory manifestations, since delayed diagnosis could lead to severe complications and even death in this group of patients. |
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Authors:
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Gholamhossein Fallahi; Mehri Najafi; Fatemeh Farhmand; Fatemeh Bazvand; Maedeh Ahmadi; Faezeh Ahmadi; Kambiz Eftekhari; Ahmad Khodad; Farzaneh Motamed; Gholamreza Khatami; Asghar Aghamohammadi; Nima Rezaei |
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Publication Detail:
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Type: Journal Article |
Journal Detail:
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Title: The Turkish journal of pediatrics Volume: 52 ISSN: 0041-4301 ISO Abbreviation: Turk. J. Pediatr. Publication Date: 2010 Mar-Apr |
Date Detail:
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Created Date: 2010-06-21 Completed Date: 2010-08-13 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 0417505 Medline TA: Turk J Pediatr Country: Turkey |
Other Details:
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Languages: eng Pagination: 132-8 Citation Subset: IM |
Affiliation:
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Department of Pediatrics, Pediatrics Center of Excellence, Children's Medical Center, Tehran, Iran. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Child Child, Preschool Consanguinity Cystic Fibrosis / diagnosis*, epidemiology, genetics, therapy Diagnosis, Differential Female Humans Infant Iran / epidemiology Male Risk Factors Young Adult |
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