Document Detail


A case with bilateral radio-ulnar synostosis.
MedLine Citation:
PMID:  18618994     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Congenital radio-ulnar synostosis may be an isolated abnormality or additional abnormalities may accompany it. It may also be found as a part of well-known syndromes. We present a case with bilateral congenital radio-ulnar synostosis, speech delay, dimple on shoulders, café au lait spot and characteristic facial appearance. The proband has a brother with similar clinical findings with the exception of congenital radio-ulnar synostosis. We discuss the possible relationship between our case and previously described syndromes with congenital radio-ulnar synostosis, and distinct phenotypic features of the presented case.
Authors:
A Koç; A O Kaymak; K Karaer; M A Ergün; T Aksu; E F Perçin
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Publication Detail:
Type:  Case Reports; Journal Article; Review    
Journal Detail:
Title:  Genetic counseling (Geneva, Switzerland)     Volume:  19     ISSN:  1015-8146     ISO Abbreviation:  Genet. Couns.     Publication Date:  2008  
Date Detail:
Created Date:  2008-07-14     Completed Date:  2008-09-09     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9015261     Medline TA:  Genet Couns     Country:  Switzerland    
Other Details:
Languages:  eng     Pagination:  193-8     Citation Subset:  IM    
Affiliation:
Department of Medical Genetics, Faculty of Medicine, Gazi University, Turkey.
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MeSH Terms
Descriptor/Qualifier:
Abnormalities, Multiple*
Child
Female
Forearm / abnormalities
Humans
Language Development Disorders
Male
Mental Retardation
Muscle Hypotonia
Radius / abnormalities*
Siblings
Synostosis*
Ulna / abnormalities*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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