Document Detail


A case of Sjögren syndrome with pulmonary amyloidosis complicating microscopic polyangiitis.
MedLine Citation:
PMID:  21437616     Owner:  NLM     Status:  Publisher    
Abstract/OtherAbstract:
We present the case of a 71-year-old Japanese woman with Sjögren syndrome complicated with pulmonary amyloidosis who developed microscopic polyangiitis. She was admitted because of fever, weight loss, and paresthesia of the plantae and fingers. Chest computed tomography revealed bilateral multiple nodules with calcification in the lung. Transbronchial lung biopsy specimens showed AL-type (primary) amyloid deposits. The patient also tested positive for myeloperoxidase-antineutrophil cytoplasmic antibodies (MPO-ANCA), with changes in the MPO-ANCA titer that paralleled changes in the symptoms. Nerve conduction velocity findings showed mononeuropathy multiplex. Livedo vasculitis was observed on bilateral lower legs, and skin biopsy showed leukoclastic vasculitis. We diagnosed the patient as having microscopic polyangiitis.
Authors:
Shin-Ya Kawashiri; Mami Tamai; Satoshi Yamasaki; Hideki Nakamura; Tomoyuki Kakugawa; Noriho Sakamoto; Yuji Ishimatsu; Atsushi Kawakami
Related Documents :
21143296 - Spectrum of skeletal abnormalities in a complex malformation syndrome with "cutis trico...
21437546 - Do you know this syndrome?
21536246 - Rasopathies: developmental disorders that predispose to cancer and skin manifestations.
4857986 - Cerebellar haemangioblastoma and genitourinary tumours.
21120186 - Jak2 v617f and the evolving paradigm of polycythemia vera.
11938406 - Delayed presentation of bilateral morgagni's hernia in a child with down's syndrome.
Publication Detail:
Type:  JOURNAL ARTICLE     Date:  2011-3-25
Journal Detail:
Title:  Modern rheumatology / the Japan Rheumatism Association     Volume:  -     ISSN:  1439-7609     ISO Abbreviation:  -     Publication Date:  2011 Mar 
Date Detail:
Created Date:  2011-3-25     Completed Date:  -     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  100959226     Medline TA:  Mod Rheumatol     Country:  -    
Other Details:
Languages:  ENG     Pagination:  -     Citation Subset:  -    
Affiliation:
Unit of Translational Medicine, Department of Immunology and Rheumatology, Graduate School of Biomedical Sciences, Nagasaki University, 1-7-1 Sakamoto, Nagasaki, 852-8501, Japan, shin-ya@hotmail.co.jp.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Five-year results of a randomised controlled multi-centre study comparing heavy-weight knitted versu...
Next Document:  Isolation and characterization of tetrachloroethylene- and cis-1,2-dichloroethylene-dechlorinating p...