| A case of severe Ebstein's anomaly with incompetent pulmonary valve. | |
| | |
MedLine Citation:
|
PMID: 12026209 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
|
A case of Ebstein's anomaly with functional pulmonary atresia diagnosed in utero is presented. The diagnosis was confirmed by postnatal echocardiographic, angiographic, and postmortem pathologic findings. On echocardiography the septal leaflet of the tricuspid valve was displaced towards the right ventricular apex. The tricuspid valve was moderately regurgitant and the arterial duct was patent. Continuous wave or color Doppler revealed serious reduction in forward flow from right ventricle through the pulmonary arteries; however, massive pulmonary regurgitation was observed. Pulmonary circulation was dependent on the ductal flow due to functional pulmonary atresia. Angiography revealed the massively enlarged right atrium, the absence of forward flow through the tricuspid valve, transfer of contrast material through the atrial septal defect to the left atrium, and the retrograde inflow of the pulmonary arteries from the aorta via the patent arterial duct. Ebstein's anomaly accompanied by functional pulmonary atresia is very rare. The fetal and neonatal presentation of this anomaly is associated with poor outcome. |
| | |
Authors:
|
Süheyla Ozkutlu; Naci Ceviz; Canan Ayabakan; Zuhal Akçören |
Related Documents
:
|
10824479 - Difference in structural change in the carpentier-edwards pericardial valves implanted ... 1703459 - Balloon valvuloplasty for fungal endocarditis induced stenosis of a bioprosthetic tricu... 1554289 - Inaccuracy of cardiac output by thermodilution during acute tricuspid regurgitation. 862449 - Pseudo-tricuspid stenosis: a rare entity. 3899649 - Diagnosis of tricuspid regurgitation. sensitivity of doppler ultrasound compared with c... 6844199 - Two-dimensional echocardiography in endomyocardial disease. 15110199 - Validation of viability assessment by electromechanical mapping by three-dimensional re... 9891579 - Abdominal and thoracoabdominal aortic aneurysm. 11392029 - Progestogens and cardiovascular disease. a critical review. |
Publication Detail:
|
Type: Case Reports; Journal Article |
Journal Detail:
|
Title: The Turkish journal of pediatrics Volume: 44 ISSN: 0041-4301 ISO Abbreviation: Turk. J. Pediatr. Publication Date: 2002 Apr-Jun |
Date Detail:
|
Created Date: 2002-05-23 Completed Date: 2002-06-11 Revised Date: 2007-11-15 |
Medline Journal Info:
|
Nlm Unique ID: 0417505 Medline TA: Turk J Pediatr Country: Turkey |
Other Details:
|
Languages: eng Pagination: 162-7 Citation Subset: IM |
Affiliation:
|
Department of Pediatrics, Hacettepe University Faculty of Medicine, Ankara, Turkey. |
Export Citation:
|
APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
|
Ebstein Anomaly
/
ultrasonography* Echocardiography Fatal Outcome Female Fetal Diseases / ultrasonography* Heart Catheterization Humans Infant, Newborn Oligohydramnios / ultrasonography Pregnancy Prenatal Diagnosis Pulmonary Atresia / ultrasonography* Pulmonary Valve / pathology, radiography, ultrasonography Tricuspid Valve / abnormalities Ultrasonography, Prenatal |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
Previous Document: Congenital double-orifice mitral valve associated with atrioventricular septal defect: a case report...
Next Document: Renal tuberculosis mimicking xanthogranulomatous pyelonephritis: ultrasonography, computed tomograph...