Document Detail


A case of antiepiligrin cicatricial pemphigoid with nephrotic syndrome.
MedLine Citation:
PMID:  15187343     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report a 71-year-old woman with antiepiligrin cicatricial pemphigoid associated with nephrotic syndrome. She presented with a six-month history of pruritic blisters over her trunk and legs. She also had episodes of recurrent painful oral erosions. A skin biopsy showed a subepidermal bulla, and a direct immunofluorescence (DIF) study revealed linear deposition of IgG and C3 at the basement membrane zone (BMZ). Indirect immunofluorescence (IIF) staining of 1 M NaCl-split skin demonstrated circulating IgG autoantibodies reactive with the dermal side. Immunoprecipitation studies of the patient's serum disclosed IgG autoantibodies directed against a set of polypeptides that corresponded to laminin 5 (beta 3 gamma 2). Based upon the long-standing edema of her legs and her hypoproteinemia, she was diagnosed with nephrotic syndrome. To our knowledge, the association of antiepiligrin cicatricial pemphigoid with nephrotic syndrome has not been reported previously.
Authors:
Yuri Uchino; Takuro Kanekura; Koichiro Takeda; Hidehiko Shimada; Mistuse Inoue; Takashi Hashimoto; Tamotsu Kanzaki
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The Journal of dermatology     Volume:  31     ISSN:  0385-2407     ISO Abbreviation:  J. Dermatol.     Publication Date:  2004 Mar 
Date Detail:
Created Date:  2004-06-09     Completed Date:  2004-07-08     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  7600545     Medline TA:  J Dermatol     Country:  Japan    
Other Details:
Languages:  eng     Pagination:  228-31     Citation Subset:  IM    
Affiliation:
Department of Dermatology, Kagoshima University Faculty of Medicine, Kagoshima, Japan.
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MeSH Terms
Descriptor/Qualifier:
Aged
Autoantibodies / immunology*
Biopsy, Needle
Cell Adhesion Molecules / immunology*
Female
Follow-Up Studies
Humans
Immunoglobulin G / analysis,  immunology
Immunohistochemistry
Japan
Nephrotic Syndrome / complications*,  diagnosis,  drug therapy,  immunology
Pemphigoid, Benign Mucous Membrane / complications*,  drug therapy,  immunology,  pathology*
Prednisone / therapeutic use
Risk Assessment
Treatment Outcome
Chemical
Reg. No./Substance:
0/Autoantibodies; 0/Cell Adhesion Molecules; 0/Immunoglobulin G; 0/kalinin; 53-03-2/Prednisone

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