Document Detail


A case of Schöpf-Schulz-Passarge syndrome.
MedLine Citation:
PMID:  16045686     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Schöpf-Schulz-Passarge syndrome (SSPS) is a rare ectodermal dysplasia characterized by hypodontia, hypotrichosis, nail dystrophy, palmoplantar keratoderma, and periocular and eyelid margin apocrine hidrocystomas. Several other skin tumours have been described in association with this syndrome, in particular, multiple palmoplantar eccrine syringofibroadenoma (ESFA). We report a case of SSPS with diffuse palmoplantar hyperkeratosis, which was shown by histology and immunocytochemistry to be due to ESFA.
Authors:
P J Hampton; B Angus; A J Carmichael
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Clinical and experimental dermatology     Volume:  30     ISSN:  0307-6938     ISO Abbreviation:  Clin. Exp. Dermatol.     Publication Date:  2005 Sep 
Date Detail:
Created Date:  2005-07-27     Completed Date:  2005-11-21     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7606847     Medline TA:  Clin Exp Dermatol     Country:  England    
Other Details:
Languages:  eng     Pagination:  528-30     Citation Subset:  IM    
Affiliation:
Pathology, Royal Victoria Infirmary, Queen Victoria Road, Newcastle upon Tyne, UK. hamptonpj@doctors.org.uk
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MeSH Terms
Descriptor/Qualifier:
Aged
Cysts / pathology
Ectodermal Dysplasia / pathology*
Eyelid Diseases / pathology
Hidrocystoma / pathology
Humans
Hypotrichosis / pathology
Keratoderma, Palmoplantar / pathology*
Male
Nail Diseases / pathology
Sweat Gland Neoplasms / pathology
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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