A case of Peutz-Jeghers syndrome with nasal polyposis, extreme iron deficiency anemia, and hamartoma-adenoma transformation: management by combined surgical and endoscopic approach. | |
MedLine Citation:
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PMID: 7639241 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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We report a rare variant of Peutz-Jeghers syndrome identified by the presence of nasal polyposis and extreme anemia. Multiple hamartomatous polyps were found throughout the upper and lower gastrointestinal tract. We conducted a combined surgical-endoscopic approach to prevent the development of a short-bowel syndrome. The polyps removed by snare and surgical polypectomy showed features typical of harmartomas. Three colonic polyps and two nasal polyps showed histological evidence of adenomatous change. This adenomatous change seems to fit into the pathogenic sequence of hamartoma-adenoma. |
Authors:
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L De Facq; J De Sutter; M De Man; P Van der Spek; L Lepoutre |
Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: The American journal of gastroenterology Volume: 90 ISSN: 0002-9270 ISO Abbreviation: Am. J. Gastroenterol. Publication Date: 1995 Aug |
Date Detail:
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Created Date: 1995-09-08 Completed Date: 1995-09-08 Revised Date: 2004-11-17 |
Medline Journal Info:
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Nlm Unique ID: 0421030 Medline TA: Am J Gastroenterol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 1330-2 Citation Subset: IM |
Affiliation:
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Department of Gastroenterology, Onze Lieve Vrouw Hospital, Aalst, Belgium. |
Export Citation:
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MeSH Terms | |
Descriptor/Qualifier:
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Adult Anemia, Iron-Deficiency / etiology* Colon / pathology Colonoscopy Combined Modality Therapy Duodenum / pathology Endoscopy, Gastrointestinal Humans Jejunum / pathology Male Nasal Polyps / complications* Peutz-Jeghers Syndrome / complications*, pathology, therapy* |
Comments/Corrections | |
Comment In:
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Am J Gastroenterol. 1996 Oct;91(10):2252-3
[PMID:
8855772
]
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From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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