Document Detail

A case of Omenn-like immunodeficiency syndrome.
MedLine Citation:
PMID:  1477428     Owner:  NLM     Status:  MEDLINE    
We report the case of a child with a variant of the Omenn immunodeficiency syndrome. He presented with erythroderma, lymphadenopathy, hepatosplenomegaly, failure to thrive, and recurrent purulent infections. The immunological studies showed marked disturbances in the subpopulations and functions of T lymphocytes, which suggests a defect in T cell differentiation as the cause of the disease.
M Morren; S Van Lierde; F Lacquet; J L Ceuppens; J Delabie; C Dewolf-Peeters; H Degreef
Related Documents :
9588648 - Streptococcus pneumoniae-induced haemolytic uraemic syndrome.
25262268 - Development of a data set of national cardiovascular deaths in the young.
6710208 - Axillary vein thrombosis simulating superior vena cava syndrome.
15330228 - Ssri-induced apathy syndrome: a clinical review.
22361458 - Corynebacterium pseudodiphtheriticum septic arthritis secondary to intra-articular inje...
8007048 - Mri manifestations of leptomeningeal metastasis.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Dermatology (Basel, Switzerland)     Volume:  185     ISSN:  1018-8665     ISO Abbreviation:  Dermatology (Basel)     Publication Date:  1992  
Date Detail:
Created Date:  1993-02-11     Completed Date:  1993-02-11     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  9203244     Medline TA:  Dermatology     Country:  SWITZERLAND    
Other Details:
Languages:  eng     Pagination:  302-4     Citation Subset:  IM    
Department of Dermatology, University Hospital, Katholieke Universiteit Leuven, Belgium.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Immunologic Deficiency Syndromes / immunology*
Lymphocyte Activation / immunology
Skin Diseases / immunology*
T-Lymphocyte Subsets / immunology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

Previous Document:  Neonatal treatment of giant naevi.
Next Document:  Genital squamous-cell carcinoma after PUVA therapy.