Document Detail


A case of Omenn-like immunodeficiency syndrome.
MedLine Citation:
PMID:  1477428     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report the case of a child with a variant of the Omenn immunodeficiency syndrome. He presented with erythroderma, lymphadenopathy, hepatosplenomegaly, failure to thrive, and recurrent purulent infections. The immunological studies showed marked disturbances in the subpopulations and functions of T lymphocytes, which suggests a defect in T cell differentiation as the cause of the disease.
Authors:
M Morren; S Van Lierde; F Lacquet; J L Ceuppens; J Delabie; C Dewolf-Peeters; H Degreef
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Dermatology (Basel, Switzerland)     Volume:  185     ISSN:  1018-8665     ISO Abbreviation:  Dermatology (Basel)     Publication Date:  1992  
Date Detail:
Created Date:  1993-02-11     Completed Date:  1993-02-11     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  9203244     Medline TA:  Dermatology     Country:  SWITZERLAND    
Other Details:
Languages:  eng     Pagination:  302-4     Citation Subset:  IM    
Affiliation:
Department of Dermatology, University Hospital, Katholieke Universiteit Leuven, Belgium.
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MeSH Terms
Descriptor/Qualifier:
Humans
Immunologic Deficiency Syndromes / immunology*
Infant
Lymphocyte Activation / immunology
Male
Skin Diseases / immunology*
T-Lymphocyte Subsets / immunology

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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