Document Detail


A case of Allgrove (Triple A) syndrome associated with renal ectopia.
MedLine Citation:
PMID:  12150219     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Allgrove syndrome (triple-A syndrome) is an autosomal recessive disorder characterized by adrenocorticotropin hormone-resistant adrenal insufficiency, achalasia and alacrima. Aside from the classic features of the syndrome, several abnormalities including mainly neurological abnormalities have been reported in the syndrome. Herein, we presented a case of Allgrove syndrome associated with left renal ectopla. To the best of our knowledge renal abnormality in Allgrove syndrome has not been reported in the literature until now. We think that ectopic kidney diagnosed in our patient is coincidental because the incidence of renal ectopia is high, approximately 1 in 900 in population.
Authors:
H Caksen; Y Cesur; E Kirimi; A Uner; S Arslan; V Celebi; O Tuncer; D Odabas
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Genetic counseling (Geneva, Switzerland)     Volume:  13     ISSN:  1015-8146     ISO Abbreviation:  Genet. Couns.     Publication Date:  2002  
Date Detail:
Created Date:  2002-08-01     Completed Date:  2003-01-03     Revised Date:  2006-07-06    
Medline Journal Info:
Nlm Unique ID:  9015261     Medline TA:  Genet Couns     Country:  Switzerland    
Other Details:
Languages:  eng     Pagination:  179-82     Citation Subset:  IM    
Affiliation:
Department of Pediatrics, Yüzüncü Yil University, Faculty of Medicine, Van, Turkey. huseyincaksen@hotmail.com
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MeSH Terms
Descriptor/Qualifier:
Adrenal Insufficiency / complications*
Child
Esophageal Achalasia / complications*
Humans
Kidney / abnormalities*
Lacrimal Apparatus Diseases / complications*
Male
Syndrome

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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