Document Detail


The benefit of targeted and selective inhibition of the alternative complement pathway for modulating autoimmunity and renal disease in MRL/lpr mice.
MedLine Citation:
PMID:  21452327     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
OBJECTIVE: Complement has both protective and pathogenic functions in lupus due to a balance between its role in the clearance of immune complexes (ICs) and apoptotic cells and its role in inflammation. The classical pathway contributes to IC and apoptotic cell clearance, whereas the alternative pathway is a key mediator of renal inflammation. The aim of this study was to investigate the effect of a new targeted inhibitor of the alternative pathway, CR2-fH, on lupus-like renal disease in MRL/lpr mice.
METHODS: Mice were treated with either saline, CR2-fH, CR2-Crry (which inhibits all complement pathways), or soluble CR2 (sCR2; C3d-binding targeting vehicle). Sera were analyzed every 2 weeks for autoantibodies, circulating ICs, and C3. Urinary excretion of albumin was also determined, and kidneys were collected at 23 weeks for histologic evaluation.
RESULTS: Treatment with CR2-fH or CR2-Crry improved survival and significantly reduced proteinuria, glomerular C3 deposition, and the level of circulating ICs. CR2-fH, but not CR2-Crry, also significantly reduced glomerulonephritis, expression of serum anti-double-stranded DNA (anti-dsDNA) antibodies, and glomerular IgG and C1q deposition. Interestingly, sCR2 also significantly reduced the levels of anti-dsDNA antibodies and circulating ICs and reduced glomerular deposition of IgG, C1q, and C3, although there was no significant reduction in glomerulonephritis, proteinuria, or mortality.
CONCLUSION: Targeted and selective inhibition of the alternative complement pathway is an effective treatment of murine lupus and is more effective than blockade of all pathways. The data demonstrate benefits to leaving the classical/lectin pathways intact and indicate distinct roles for the classical and alternative pathways of complement in disease progression. The sCR2-targeting vehicle contributes to therapeutic activity, possibly via modulation of autoimmunity.
Authors:
Hideharu Sekine; Ting Ting Hsieh Kinser; Fei Qiao; Efrain Martinez; Emily Paulling; Phillip Ruiz; Gary S Gilkeson; Stephen Tomlinson
Related Documents :
1715357 - Lead and immunity: ii. suppression of humoral immune response to hymenolepis nana in mice.
6981507 - Acute phase proteins, humoral and cell mediated immunity in environmentally-induced hyp...
365757 - Role of bacterial products in periodontitis: humoral immune response to eikenella corro...
21155967 - Complement in atherosclerosis - friend or foe?
3002397 - Effects of gold sodium thiomalate on functional correlates of human monocyte maturation.
9152987 - Inhibition of the interleukin-1 beta converting enzyme family rescues neurons from apop...
Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, U.S. Gov't, Non-P.H.S.    
Journal Detail:
Title:  Arthritis and rheumatism     Volume:  63     ISSN:  1529-0131     ISO Abbreviation:  Arthritis Rheum.     Publication Date:  2011 Apr 
Date Detail:
Created Date:  2011-03-31     Completed Date:  2011-05-23     Revised Date:  2012-04-04    
Medline Journal Info:
Nlm Unique ID:  0370605     Medline TA:  Arthritis Rheum     Country:  United States    
Other Details:
Languages:  eng     Pagination:  1076-85     Citation Subset:  AIM; IM    
Copyright Information:
Copyright © 2011 by the American College of Rheumatology.
Affiliation:
Medical University of South Carolina, Charleston, SC, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Animals
Antibodies, Anti-Idiotypic / blood
Antigen-Antibody Complex / blood
Autoimmunity / drug effects*,  physiology
Complement C1q / metabolism
Complement C3 / metabolism
Complement Inactivating Agents / pharmacology*,  therapeutic use*
Complement Pathway, Alternative / drug effects*,  physiology
DNA / immunology
Disease Models, Animal
Female
Immunoglobulin G / blood
Kidney / drug effects,  pathology
Kidney Diseases / drug therapy*,  etiology,  immunology
Lupus Erythematosus, Systemic / complications,  drug therapy*,  immunology
Mice
Mice, Inbred MRL lpr
Recombinant Fusion Proteins / pharmacology
Grant Support
ID/Acronym/Agency:
HL-082485/HL/NHLBI NIH HHS; R01 HL082485-04/HL/NHLBI NIH HHS; R01 HL086576-04/HL/NHLBI NIH HHS
Chemical
Reg. No./Substance:
0/Antibodies, Anti-Idiotypic; 0/Antigen-Antibody Complex; 0/CR2-Crry fusion protein, mouse; 0/Complement C3; 0/Complement Inactivating Agents; 0/Immunoglobulin G; 0/Recombinant Fusion Proteins; 80295-33-6/Complement C1q; 9007-49-2/DNA

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Fracture risk before and after total hip replacement in patients with osteoarthritis: Potential bene...
Next Document:  Cluster analysis of arterial involvement in Takayasu arteritis reveals symmetric extension of the le...