Document Detail

The anaesthetic management of an infant with frontometaphyseal dysplasia (Gorlin-Cohen syndrome).
MedLine Citation:
PMID:  3176838     Owner:  NLM     Status:  MEDLINE    
We describe an infant with frontometaphyseal dysplasia, who presented to us twice for anaesthesia for orthopaedic surgery. These patients have facial asymmetry, mandibular hypoplasia, bradycardia, restrictive lung disease, primary pulmonary hypertension, skeletal abnormalities and difficult endotracheal intubation. The patient also showed laryngeal stridor because of laryngomalacia, vocal cord paralysis and subglottic stenosis. Light premedication along with atropine, ECG and blood pressure monitoring, gradual inhalational induction and intubation of the spontaneously breathing patient, careful positioning and postoperative CPAP are recommended.
Y Mehta; H Schou
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Acta anaesthesiologica Scandinavica     Volume:  32     ISSN:  0001-5172     ISO Abbreviation:  Acta Anaesthesiol Scand     Publication Date:  1988 Aug 
Date Detail:
Created Date:  1988-11-23     Completed Date:  1988-11-23     Revised Date:  2006-11-15    
Medline Journal Info:
Nlm Unique ID:  0370270     Medline TA:  Acta Anaesthesiol Scand     Country:  DENMARK    
Other Details:
Languages:  eng     Pagination:  505-7     Citation Subset:  IM    
Department of Anaesthesia, Odense University Hospital, Denmark.
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MeSH Terms
Abnormalities, Multiple / pathology
Anesthesia, Inhalation*
Bone Diseases, Developmental / pathology*
Face / abnormalities*
Nitrous Oxide
Respiratory Sounds
Skull / abnormalities*
Reg. No./Substance:
10024-97-2/Nitrous Oxide; 151-67-7/Halothane

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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