| Xanthoma disseminatum. An unusual histiocytosis syndrome. | |
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MedLine Citation:
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PMID: 3140686 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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The histiocytoses are a diverse group of illnesses that present a variety of diagnostic and therapeutic dilemmas. In this article, we describe the case of an 8-year-old boy with xanthoma disseminatum, a histiocytic disorder involving the skin, eyes, and brain. In our discussion, we have emphasized the clinical, pathologic, and radiographic features that distinguish this entity from clinically similar juvenile xanthogranuloma and Langerhans' cell histiocytoses (histiocytosis X) such as the Hand-Schuller-Christian syndrome. The importance of differentiating the various histiocytoses, in view of their varying natural histories and therapeutic responsiveness, is reviewed in relation to the new classification system for these disorders proposed by the Histiocyte Society. |
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Authors:
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R H Giller; R Folberg; R V Keech; W W Piette; Y Sato |
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Publication Detail:
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Type: Case Reports; Comparative Study; Journal Article; Research Support, Non-U.S. Gov't |
Journal Detail:
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Title: The American journal of pediatric hematology/oncology Volume: 10 ISSN: 0192-8562 ISO Abbreviation: Am J Pediatr Hematol Oncol Publication Date: 1988 |
Date Detail:
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Created Date: 1988-11-16 Completed Date: 1988-11-16 Revised Date: 2006-11-15 |
Medline Journal Info:
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Nlm Unique ID: 7908071 Medline TA: Am J Pediatr Hematol Oncol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 252-7 Citation Subset: IM |
Affiliation:
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Department of Pediatrics, University of Iowa College of Medicine, Iowa City. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Brain Diseases
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diagnosis Child Diagnosis, Differential Eye Diseases / diagnosis Histiocytosis, Langerhans-Cell / diagnosis Humans Male Syndrome Xanthogranuloma, Juvenile / diagnosis Xanthomatosis / classification, diagnosis* |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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