Document Detail


Wildervanck's syndrome--unilateral Mondini dysplasia identified by computed tomography.
MedLine Citation:
PMID:  2715696     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We present a case of the Wildervanck (cervico-oculo-acoustic) syndrome exhibiting congenital deafness. Klippel-Feil anomaly and lateral rectus palsy with enophthalmos. Audiometry indicated a predominantly conductive loss which, because of masking difficulties, was assumed to be bilateral: an erroneous assumption supported by results of conventional petrous bone tomography which failed to demonstrate any abnormality of the inner ears. Computed tomography (CT), however, revealed a severe Mondini dysplasia of one ear, a condition which must be assumed to be associated with severe sensorineural hearing loss. Reconstructive middle ear surgery for the conductive loss on the other side was therefore contraindicated.
Authors:
P D West; A Gholkar; R T Ramsden
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The Journal of laryngology and otology     Volume:  103     ISSN:  0022-2151     ISO Abbreviation:  J Laryngol Otol     Publication Date:  1989 Apr 
Date Detail:
Created Date:  1989-06-21     Completed Date:  1989-06-21     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  8706896     Medline TA:  J Laryngol Otol     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  408-11     Citation Subset:  AIM; IM    
Affiliation:
Department of Otolaryngology, Manchester Royal Infirmary.
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MeSH Terms
Descriptor/Qualifier:
Child, Preschool
Cochlea / abnormalities*,  radiography
Deafness / congenital*
Duane Retraction Syndrome / complications*
Humans
Klippel-Feil Syndrome / complications*
Male
Ophthalmoplegia / complications*
Syndrome
Tomography, X-Ray Computed*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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