Document Detail


Why do cone photoreceptors die in rod-specific forms of retinal degenerations?
MedLine Citation:
PMID:  19941421     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Retinal degenerations such as retinitis pigmentosa (RP) lead to rod death due to apoptotic cell death, initiated by mutations in retinal genes that encode proteins with crucial photoreceptors functions. The mechanism(s) of cone death have remained elusive until this study. Using a combination of animal models of human RP, Affymetrix expression array studies, RT-PCR and immunohistochemical analyses, Punzo et al. determined that cone death is due to nutritional deficiencies, starration, and autophagy driven by the insulin/mTOR pathway. These novel and exciting seights also provide alternative avenues for therapeutic interventions for cone rescue.
Authors:
Robert K Koenekoop
Publication Detail:
Type:  Journal Article; Review    
Journal Detail:
Title:  Ophthalmic genetics     Volume:  30     ISSN:  1744-5094     ISO Abbreviation:  Ophthalmic Genet.     Publication Date:  2009 Sep 
Date Detail:
Created Date:  2009-11-27     Completed Date:  2010-02-16     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9436057     Medline TA:  Ophthalmic Genet     Country:  England    
Other Details:
Languages:  eng     Pagination:  152-4     Citation Subset:  IM    
Affiliation:
McGill Ocular Genetics Laboratory, McGill University Health Center, Montreal, Quebec, Canada. robert.koenekoop@mcgill.ca
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MeSH Terms
Descriptor/Qualifier:
Animals
Apoptosis*
Autophagy
Humans
Retinal Cone Photoreceptor Cells / pathology*
Retinal Rod Photoreceptor Cells / pathology*
Retinitis Pigmentosa / pathology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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