Document Detail


Waardenburg syndrome type I with heterochromia iridis and circumscribed hypopigmentation of the skin.
MedLine Citation:
PMID:  20199465     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
We report a 3-year-old girl with autosomal dominant inherited Waardenburg syndrome type I showing circumscribed hypopigmentation of the skin, heterochromia iridis, sensorineural deafness, and dental aberrations. Clinical diagnosis was confirmed by the identification of an underlying missense mutation (C811T) in the PAX3 gene. Early diagnosis of Waardenburg syndrome among children with pigment anomalies enables a successful interdisciplinary medical care.
Authors:
Sibylle Eigelshoven; Gitta Kameda; Anne-Katrin Kort?m; Simone H?bsch; Wolfgang Angerstein; Preeti Singh; Renate V?hringer; Timm Goecke; Ertan Mayatepek; Thomas Ruzicka; Gabriele Wildhardt; Thomas Meissner; Roland Kruse
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Pediatric dermatology     Volume:  26     ISSN:  1525-1470     ISO Abbreviation:  Pediatr Dermatol     Publication Date:    2009 Nov-Dec
Date Detail:
Created Date:  2010-03-04     Completed Date:  2010-06-02     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  8406799     Medline TA:  Pediatr Dermatol     Country:  United States    
Other Details:
Languages:  eng     Pagination:  759-61     Citation Subset:  IM    
Affiliation:
Department of Dermatology, Heinrich-Heine-University, D?sseldorf, Germany. Eigelshoven@med.uni-duesseldorf.de
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MeSH Terms
Descriptor/Qualifier:
Anodontia / genetics,  pathology
Child, Preschool
Female
Hearing Loss, Sensorineural / genetics,  pathology
Humans
Hypopigmentation / genetics,  pathology*
Iris Diseases / genetics,  pathology*
Mutation, Missense
Paired Box Transcription Factors / genetics
Waardenburg's Syndrome / genetics,  pathology*
Chemical
Reg. No./Substance:
0/PAX3 protein, human; 0/Paired Box Transcription Factors

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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