Document Detail


WHIM syndrome and oral squamous cell carcinoma.
MedLine Citation:
PMID:  19926501     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
WHIM (warts, hypogammaglobulinemia, infections, and myelokathexis) syndrome is an autosomal dominant disease related to a mutation in the chemokine receptor CXCR4 resulting in altered immune function. An increased susceptibility in these patients to human papillomavirus (HPV) manifests as cutaneous warts and, in women, cervical dysplasia and squamous carcinoma. HPV-related squamous carcinoma in other sites has not been documented. We report the occurrence of HPV-related squamous cell carcinoma of the oral cavity in 2 siblings with WHIM syndrome, whose pedigree has previously been described.
Authors:
Nicole A Cipriani; Elizabeth Blair; Jerome B Taxy
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Oral surgery, oral medicine, oral pathology, oral radiology, and endodontics     Volume:  109     ISSN:  1528-395X     ISO Abbreviation:  Oral Surg Oral Med Oral Pathol Oral Radiol Endod     Publication Date:  2010 Jan 
Date Detail:
Created Date:  2010-02-03     Completed Date:  2010-04-19     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9508562     Medline TA:  Oral Surg Oral Med Oral Pathol Oral Radiol Endod     Country:  United States    
Other Details:
Languages:  eng     Pagination:  105-8     Citation Subset:  D; IM    
Copyright Information:
Copyright 2010 Mosby, Inc. All rights reserved.
Affiliation:
Department of Pathology, University of Chicago Medical Center, Chicago, Illinois 60637, USA. nicole.cipriani@uchospitals.edu
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MeSH Terms
Descriptor/Qualifier:
Adult
Agammaglobulinemia / complications*,  immunology
Bacterial Infections / complications,  immunology
Bone Marrow Cells / pathology
Carcinoma, Squamous Cell / etiology*
Female
Humans
Immunohistochemistry
Male
Middle Aged
Mouth Neoplasms / etiology*
Neoplasm Proteins / analysis
Siblings
Syndrome
Warts / complications*,  immunology
Chemical
Reg. No./Substance:
0/Neoplasm Proteins; 0/P16 protein, human

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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