Document Detail


Vulvar congenital dysplastic angiopathy.
MedLine Citation:
PMID:  2154731     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Congenital dysplastic angiopathy is a syndrome consisting of vascular angiomata, congenital varicosities, and trophic changes of the soft tissue and the skeleton. Frequently referred to as Klippel-Trenaunay or Klippel-Trenaunay-Weber syndrome, it rarely affects the female genitalia. An 18-year-old woman underwent evaluation and treatment for Klippel-Trenaunay syndrome with vulvar involvement. Preoperative evaluation included consultation with pediatric surgeons, gynecologic surgeons, and an interventional radiologist as well as individual and family psychological counseling. Attention to intraoperative detail resulted in minimal operative blood loss and preservation of normal anatomy. A postoperative hematoma was treated aggressively with surgical evacuation and drainage. Six-month follow-up revealed functionally and cosmetically normal vulvar anatomy.
Authors:
B L Tjaden; J Buscema; J A Haller; J A Rock
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Obstetrics and gynecology     Volume:  75     ISSN:  0029-7844     ISO Abbreviation:  Obstet Gynecol     Publication Date:  1990 Mar 
Date Detail:
Created Date:  1990-03-20     Completed Date:  1990-03-20     Revised Date:  2009-10-26    
Medline Journal Info:
Nlm Unique ID:  0401101     Medline TA:  Obstet Gynecol     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  552-4     Citation Subset:  AIM; IM    
Affiliation:
Department of Gynecology and Obstetrics, Johns Hopkins University, Baltimore, Maryland.
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MeSH Terms
Descriptor/Qualifier:
Adolescent
Female
Hemangioma* / congenital,  pathology,  surgery
Humans
Klippel-Trenaunay-Weber Syndrome / pathology
Methods
Postoperative Complications
Vulva / surgery
Vulvar Neoplasms* / congenital,  pathology,  surgery

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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