Document Detail


Visual rehabilitation in a child with diffuse choroidal hemangioma by using aggressive amblyopia therapy with low-dose external beam irradiation.
MedLine Citation:
PMID:  11040486     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Diffuse choroidal hemangioma is a congenital vascular hamartoma often associated with hemangiomatous lesions of the brain, orbit, and periocular skin (nevus flammeus) in the Sturge-Weber syndrome. Visual loss from diffuse choroidal hemangioma may result from chronic serous retinal detachments causing retinal pigment epithelial, photoreceptor or cystoid degeneration, and glaucomatous optic atrophy. Low-dose external beam irradiation has successfully resolved exudative retinal detachment and caused shrinkage of the choroidal hemangioma.(1-3) Visual loss in Sturge-Weber syndrome with diffuse choroidal hemangioma often begins during amblyogenic years. Visual rehabilitation may thus require not only therapeutic intervention to address organic disease but also amblyopia therapy. Though many of the previously reported cases address treatment of the diffuse choroidal hemangioma with laser or radiotherapy, none advocate or emphasize treatment of nonorganic amblyopia associated with this condition. We report the case of a child with Sturge-Weber syndrome and unilateral diffuse submacular choroidal hemangioma who developed an exudative retinal detachment that responded to the combination of low-dose external beam irradiation and aggressive amblyopia therapy.
Authors:
E A Packwood; S A Havertape; O A Cruz; E S Mann
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus / American Association for Pediatric Ophthalmology and Strabismus     Volume:  4     ISSN:  1091-8531     ISO Abbreviation:  J AAPOS     Publication Date:  2000 Oct 
Date Detail:
Created Date:  2000-11-22     Completed Date:  2000-12-07     Revised Date:  2006-04-21    
Medline Journal Info:
Nlm Unique ID:  9710011     Medline TA:  J AAPOS     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  321-2     Citation Subset:  IM    
Affiliation:
Department of Ophthalmology, Saint Louis University School of Medicine, St Louis, Missouri 63104, USA.
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MeSH Terms
Descriptor/Qualifier:
Amblyopia / etiology,  physiopathology,  rehabilitation*
Child
Choroid Neoplasms / complications,  physiopathology,  radiotherapy*
Eyeglasses*
Hemangioma / complications,  physiopathology,  radiotherapy*
Humans
Male
Sensory Deprivation*
Visual Acuity / physiology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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