| Vasoactive intestinal polypeptide-producing ganglioneuromatosis involving the entire colon and rectum. | |
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MedLine Citation:
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PMID: 19302839 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Vasoactive intestinal polypeptide (VIP) is known to cause the watery diarrhea, hypokalemia, and achlorhydria syndrome. A 14-year-old girl was admitted with a 4-year history of persistent uncontrollable diarrhea and hypokalemia. Computed tomographic evaluation of the neck, chest, and abdomen were normal. Numerous polyps covering the entire colon and rectum were noted on colonoscopy. The serum VIP level was 143 pg/mL. The patient underwent a total proctocolectomy with an ileal-J-pouch. The pathologic examination revealed ganglioneuromatosis. Postoperatively, the symptoms resolved, and the serum VIP level fell to lower than 5 pg/mL. This is an unusual case of the watery diarrhea, hypokalemia, and achlorhydria syndrome caused by ganglioneuromatosis of the entire colon and rectum. |
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Authors:
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Suk-Bae Moon; Kwi-Won Park; Sung-Eun Jung; Seong-Cheol Lee |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: Journal of pediatric surgery Volume: 44 ISSN: 1531-5037 ISO Abbreviation: J. Pediatr. Surg. Publication Date: 2009 Mar |
Date Detail:
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Created Date: 2009-03-23 Completed Date: 2009-07-15 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 0052631 Medline TA: J Pediatr Surg Country: United States |
Other Details:
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Languages: eng Pagination: e19-21 Citation Subset: IM |
Affiliation:
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Department of Pediatric Surgery, Seoul National University Children's Hospital, Seoul 110-744, Korea. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adolescent Colonic Neoplasms / metabolism*, surgery Colonic Pouches Female Ganglioneuroma / metabolism*, surgery Humans Proctocolectomy, Restorative Rectal Neoplasms / metabolism* Vasoactive Intestinal Peptide / blood, metabolism* |
| Chemical | |
Reg. No./Substance:
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37221-79-7/Vasoactive Intestinal Peptide |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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