Document Detail


Useful residual hearing despite radiological findings suggestive of anacusis.
MedLine Citation:
PMID:  10748844     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
A severe malformation of the inner ear, often referred to as severe labyrinthine dysplasia or common cavity deformity, consists of an absent or dilated cochlear basal coil, wide communication with the vestibule and a tapered internal acoustic meatus and can be associated with absent hearing. We discuss two children with severe labyrinthine dysplasia as shown by computed tomography (CT) scans and, in the first case, an absent VIIIth nerve bilaterally shown by magnetic resonance imaging (MRI). In 1995, both cases were precluded from cochlear implantation, on the basis of the absent VIIIth nerve (first case) and increased risk of CSF leak during operation (second case). However, audiometric results and vocalization patterns of both children suggested the presence of some residual hearing function, while recently reported specific surgical techniques have been found to be safe and effective in the cochlear implantation of the common cavity deformity. The management of such cases should be decided on the grounds of a full audiological assessment in conjunction with the radiological features, in the light of current surgical trends shown to be safe and effective.
Authors:
D E Bamiou; C O Mahoney; T Sirimanna
Related Documents :
12618204 - Fibrous dysplasia in the maxilla: possible mechanism of bone remodeling by calcitonin t...
3201274 - Osteofibrous dysplasia. a report of two cases.
18816444 - Absence of the long head of the biceps tendon associated with glenoid dysplasia and pos...
3297114 - Cellular neurothekeoma.
20519804 - Giant fibroadenoma in a 22 year old patient: case report and literature review.
8515764 - Latex hypersensitivity following exposure to gloves during electromyography.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  The Journal of laryngology and otology     Volume:  113     ISSN:  0022-2151     ISO Abbreviation:  J Laryngol Otol     Publication Date:  1999 Aug 
Date Detail:
Created Date:  2000-04-25     Completed Date:  2000-04-25     Revised Date:  2005-11-17    
Medline Journal Info:
Nlm Unique ID:  8706896     Medline TA:  J Laryngol Otol     Country:  ENGLAND    
Other Details:
Languages:  eng     Pagination:  714-6     Citation Subset:  AIM; IM    
Affiliation:
Audiology Department, Great Ormond Street Hospital, London, UK. doriseva@ndirect.co.uk
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Audiometry, Evoked Response
Audiometry, Pure-Tone
Cochlear Implantation / contraindications*
Ear, Inner / abnormalities*,  radiography
Female
Hearing Disorders / etiology
Hearing Loss, Bilateral / congenital*,  rehabilitation
Humans
Infant
Magnetic Resonance Imaging
Tomography, X-Ray Computed
Vestibulocochlear Nerve / abnormalities*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  Radical revision mastoidectomy for chronic otitis media without cholesteatoma: the relevance of exce...
Next Document:  Subtemporal exposure of the intrapetrous internal carotid artery. An anatomical study with surgical ...