| Upper airway obstruction in Sturge-Weber and Klippel-Trenaunay-Weber syndromes. | |
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MedLine Citation:
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PMID: 7747906 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Sturge-Weber syndrome is a rare congenital angiomatosis of unknown cause that is defined by the following triad: facial port-wine stain, leptomeningeal vascular anomalies, and choroidal vascular lesions associated with glaucoma. Klippel-Trenaunay-Weber syndrome is a related disease with questionable hereditary factors diagnosed by the following triad: superficial nevus of the lower extremity, ipsilateral varicose veins, and hypertrophy of the soft and bony tissues of the lower limb. The two conditions rarely have been reported to coexist. Upper airway obstruction is not a prominent feature of either of these two diseases. We present two patients with both of these angiomatoses in whom severe upper airway obstruction necessitated tracheotomy. |
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Authors:
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D S Reich; B J Wiatrak |
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Publication Detail:
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Type: Case Reports; Journal Article |
Journal Detail:
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Title: The Annals of otology, rhinology, and laryngology Volume: 104 ISSN: 0003-4894 ISO Abbreviation: Ann. Otol. Rhinol. Laryngol. Publication Date: 1995 May |
Date Detail:
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Created Date: 1995-06-14 Completed Date: 1995-06-14 Revised Date: 2006-05-15 |
Medline Journal Info:
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Nlm Unique ID: 0407300 Medline TA: Ann Otol Rhinol Laryngol Country: UNITED STATES |
Other Details:
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Languages: eng Pagination: 364-8 Citation Subset: AIM; IM |
Affiliation:
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Division of Otolaryngology, Children's Hospital of Alabama at Birmingham 35233, USA. |
Export Citation:
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APA/MLA Format Download EndNote Download BibTex |
| MeSH Terms | |
Descriptor/Qualifier:
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Airway Obstruction
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diagnosis,
etiology*,
surgery Brain / pathology*, radiography Bronchoscopy Calcinosis / pathology Child Humans Klippel-Trenaunay-Weber Syndrome / complications, diagnosis, pathology* Laryngoscopy Male Maxilla / pathology*, surgery Palate / pathology*, surgery Seizures / complications Sturge-Weber Syndrome / complications, diagnosis, pathology* Tomography, X-Ray Computed Tracheotomy |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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