Document Detail

Unusual retinal and renal vascular lesions in the Klippel-Trenaunay-Weber syndrome.
MedLine Citation:
PMID:  1336616     Owner:  NLM     Status:  MEDLINE    
Ocular fundus abnormalities associated with the Klippel-Trenaunay-Weber syndrome are uncommon and include retinal vascular tortuosity and diffuse choroidal hemangioma. A case involving a young girl with Klippel-Trenaunay-Weber syndrome who had unusual bilateral, exudative, outer retinal vascular masses involving the peripheral fundus in one eye and the foveal area in the other eye is reported. Kidney biopsy for renal insufficiency disclosed abnormal excess mesangial tissue. The fundus lesions appear to represent vascular tumors of the retina that differ clinically from previously reported retinal vascular tumors and Coats disease. The simultaneous retinal and renal involvement suggest that Klippel-Trenaunay-Weber syndrome may be associated with more widespread vascular malformations than previously realized.
R D Brod; J A Shields; C L Shields; O R Oberkircher; L J Sabol
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Publication Detail:
Type:  Case Reports; Journal Article; Research Support, Non-U.S. Gov't    
Journal Detail:
Title:  Retina (Philadelphia, Pa.)     Volume:  12     ISSN:  0275-004X     ISO Abbreviation:  Retina (Philadelphia, Pa.)     Publication Date:  1992  
Date Detail:
Created Date:  1993-02-18     Completed Date:  1993-02-18     Revised Date:  2006-12-15    
Medline Journal Info:
Nlm Unique ID:  8309919     Medline TA:  Retina     Country:  UNITED STATES    
Other Details:
Languages:  eng     Pagination:  355-8     Citation Subset:  IM    
Department of Ophthalmology, Geisinger Medical Center, Danville, Pennsylvania.
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MeSH Terms
Exudates and Transudates
Fluorescein Angiography
Fundus Oculi
Infant, Newborn
Klippel-Trenaunay-Weber Syndrome / pathology*
Retinal Diseases / pathology
Retinal Vessels / pathology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

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