Document Detail


Two puzzling cases of thyroid dysgenesis.
MedLine Citation:
PMID:  19153515     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
BACKGROUND: In the last couple of years, different genes that play major roles in embryonic thyroid development have been identified. Several mutations, e.g., NKX2.1, FOXE1 and PAX8, were identified in patients with congenital hypothyroidism due to thyroid dysgenesis. However, the pathophysiology of most cases of thyroid dysgenesis remains unknown. Due to the sporadic occurrence and discordance observed in monozygotic twins, a classic genetic hypothesis for thyroid dysgenesis is improbable. CASE REPORT: We present two pairs of monozygotic twins discordant for thyroid dysgenesis that exemplify these conceptual difficulties. CONCLUSIONS: Identification of the epigenetic differences observed in monozygotic twins discordant for thyroid dysgenesis may be crucial in discovering the pathogenesis of thyroid dysgenesis.
Authors:
P Kuehnen; A Grueters; H Krude
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Publication Detail:
Type:  Case Reports; Journal Article     Date:  2009-01-21
Journal Detail:
Title:  Hormone research     Volume:  71 Suppl 1     ISSN:  1423-0046     ISO Abbreviation:  Horm. Res.     Publication Date:  2009 Jan 
Date Detail:
Created Date:  2009-01-20     Completed Date:  2009-04-16     Revised Date:  2009-10-23    
Medline Journal Info:
Nlm Unique ID:  0366126     Medline TA:  Horm Res     Country:  Switzerland    
Other Details:
Languages:  eng     Pagination:  93-7     Citation Subset:  IM    
Copyright Information:
Copyright 2009 S. Karger AG, Basel.
Affiliation:
Institute of Experimental Paediatric Endocrinology, Charité, Berlin, Germany.
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MeSH Terms
Descriptor/Qualifier:
Child
Child, Preschool
Congenital Hypothyroidism / diagnosis,  etiology
Diseases in Twins / diagnosis
Female
Humans
Male
Thyroid Dysgenesis / complications,  diagnosis*
Thyroid Gland / ultrasonography
Twins, Monozygotic*
Comments/Corrections
Comment In:
Horm Res. 2009;72(5):320   [PMID:  19844119 ]

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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