Document Detail


Two different anesthetic managements of a patient with von Gierke's disease.
MedLine Citation:
PMID:  16623410     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Von Gierke's disease, a form of glycogen storage disturbance, is a rare metabolic disorder with important implications for anesthesiologists. It is caused by the lack of the glucose-6-phosphatase, which is necessary for the liver to convert glycogen to glucose. To avoid severe hypoglycemia, it is crucial to keep oral feeding at intervals 2-3 hr for maintaining a normal blood sugar level. The metabolic derangements of von Gierke's disease may result in serious complications in patients undergoing surgery and anesthesia. We report the anesthetic managements of a patient with von Gierke's disease in two operations with different encounters.
Authors:
I-Ren Huang; Wei-Horng Jean; Cheng-Wei Lu; Chia-Chan Wu; Tzu-Yu Lin; Yueh-Hsun Chuang; Wei-Zen Sun
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Acta anaesthesiologica Taiwanica : official journal of the Taiwan Society of Anesthesiologists     Volume:  44     ISSN:  1875-4597     ISO Abbreviation:  -     Publication Date:  2006 Mar 
Date Detail:
Created Date:  2006-04-20     Completed Date:  2006-05-25     Revised Date:  2008-04-07    
Medline Journal Info:
Nlm Unique ID:  101214918     Medline TA:  Acta Anaesthesiol Taiwan     Country:  China (Republic : 1949- )    
Other Details:
Languages:  eng     Pagination:  51-3     Citation Subset:  IM    
Affiliation:
Department of Anesthesiology, Far Eastern Memorial Hospital, Pan-Chiao, Taipei, Taiwan, ROC.
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MeSH Terms
Descriptor/Qualifier:
Adult
Anesthesia / methods*
Blood Glucose / analysis
Glycogen Storage Disease Type I / metabolism*
Humans
Male
Chemical
Reg. No./Substance:
0/Blood Glucose

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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