Document Detail

Two cases of atypical membranous aplasia cutis with hair collar sign: one with dermal melanocytosis, and the other with naevus flammeus.
MedLine Citation:
PMID:  16045676     Owner:  NLM     Status:  MEDLINE    
We report two atypical cases of membranous aplasia cutis surrounded by a rim of hairs, one case associated with dense dermal melanocytosis and the other with naevus flammeus, with characteristic clinical features. A rim of hypertrichosis, 'hair collar' sign, is proposed to have a close association with neuroectodermal defects. A failure of the normal closure of the cranial neural tube might have affected foetal skin development, including melanoblast migration and capillary network formation. The changes in the present cases, as well as the hair collar sign may suggest a complex hamartomatous nature of membranous aplasia cutis.
Y Fujita; K Yokota; M Akiyama; S Machino; D Inokuma; K Arita; C Kimura; H Shimizu
Related Documents :
6740506 - Lateral cephalothoracopagus: a case report.
11522176 - The tessier number 5 cleft with associated extremity anomalies.
11579866 - The ibadan conjoined twins: a report of omphalopagus twins and a review of cases report...
3550066 - Sonographic findings in the prenatal diagnosis of cephalothoracopagus syncephalus. a ca...
16214206 - Rhabdomyosarcoma of the cervix in sisters with review of the literature.
19458136 - Successful treatment of extreme acute lead intoxication.
Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Clinical and experimental dermatology     Volume:  30     ISSN:  0307-6938     ISO Abbreviation:  Clin. Exp. Dermatol.     Publication Date:  2005 Sep 
Date Detail:
Created Date:  2005-07-27     Completed Date:  2005-11-21     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  7606847     Medline TA:  Clin Exp Dermatol     Country:  England    
Other Details:
Languages:  eng     Pagination:  497-9     Citation Subset:  IM    
Department of Plastic Surgery, Hakodate Central General Hospital, Hakodate, Japan.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Ectodermal Dysplasia / pathology*
Hypertrichosis / pathology*
Melanosis / pathology*
Port-Wine Stain / pathology*
Scalp Dermatoses / pathology*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine

Previous Document:  Dyschromatosis universalis hereditaria: two cases in a Chinese family.
Next Document:  Persistent severe amiodarone-induced photosensitivity.