Document Detail


Tricuspid atresia with absent pulmonary valve and intact ventricular septum: intrauterine course and outcome of an unusual congenital heart defect.
MedLine Citation:
PMID:  20069575     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
The extremely rare syndrome including absent pulmonary valve associated with membranous tricuspid atresia or severe tricuspid stenosis, intact ventricular septum and patent ductus arteriosus has been reported sporadically in the postnatal literature. This cardiac defect is characterized by right ventricular dysplasia with asymmetrical ventricular septal hypertrophy, ventricular septum bulging into the left ventricle, small right ventricular cavity, membranous tricuspid atresia or severe stenosis with abnormal papillary muscles and leaflets and absence of the pulmonary valve leaflets. The only prenatal case reported so far was diagnosed at 33 weeks of gestation and terminated shortly thereafter; the natural history of prenatally diagnosed cases is therefore unknown. We report on the intrauterine course of a case diagnosed at 17 weeks of gestation that had a favorable postnatal outcome after palliation.
Authors:
K Lato; U Gembruch; A Geipel; R Lachmann; M Schneider; V Hraska; C Berg
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and Gynecology     Volume:  35     ISSN:  1469-0705     ISO Abbreviation:  Ultrasound Obstet Gynecol     Publication Date:  2010 Feb 
Date Detail:
Created Date:  2010-02-01     Completed Date:  2010-09-14     Revised Date:  -    
Medline Journal Info:
Nlm Unique ID:  9108340     Medline TA:  Ultrasound Obstet Gynecol     Country:  England    
Other Details:
Languages:  eng     Pagination:  243-5     Citation Subset:  IM    
Affiliation:
Department of Obstetrics and Prenatal Medicine, University of Bonn, Bonn, Germany.
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MeSH Terms
Descriptor/Qualifier:
Adult
Aneurysm / embryology,  surgery,  ultrasonography
Female
Fetal Heart / ultrasonography*
Heart Septal Defects, Ventricular / embryology,  surgery,  ultrasonography*
Humans
Infant, Newborn
Male
Pregnancy
Pregnancy Outcome
Pulmonary Artery / embryology,  surgery,  ultrasonography
Pulmonary Valve / abnormalities*,  embryology
Tricuspid Atresia / embryology,  pathology,  ultrasonography*
Ultrasonography, Prenatal

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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