| Tricuspid valve dysplasia with severe tricuspid regurgitation: fetal pulmonary artery size predicts lung viability in the presence of small lung volumes. | |
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MedLine Citation:
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PMID: 20090295 Owner: NLM Status: MEDLINE |
Abstract/OtherAbstract:
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Congenital tricuspid valve disease (Ebstein's anomaly, tricuspid valve dysplasia) with severe tricuspid regurgitation and cardiomegaly is associated with poor prognosis. Fetal echocardiography can accurately measure right atrial enlargement, which is associated with a poor prognosis in the fetus with tricuspid valve disease. Fetal lung volumetric assessments have been used in an attempt to predict viability of fetuses using ultrasonogram and prenatal MRI. We describe a fetus with tricuspid dysplasia, severe tricuspid regurgitation, right atrial enlargement and markedly reduced lung volumes. The early gestational onset of cardiomegaly with bilateral lung compression raised the possibility of severe lung hypoplasia with decreased broncho-alveolar development. Use of fetal echocardiography with measurement of pulmonary artery size combined with prenatal MRI scanning of lung volumes resulted in an improved understanding of this anomaly and directed the management strategy towards a successful Fontan circulation. |
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Authors:
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A T Nathan; B S Marino; T Dominguez; S Tabbutt; S Nicolson; D D Donaghue; T L Spray; J Rychik |
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Publication Detail:
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Type: Case Reports; Journal Article Date: 2010-01-12 |
Journal Detail:
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Title: Fetal diagnosis and therapy Volume: 27 ISSN: 1421-9964 ISO Abbreviation: Fetal. Diagn. Ther. Publication Date: 2010 |
Date Detail:
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Created Date: 2010-03-24 Completed Date: 2010-06-10 Revised Date: - |
Medline Journal Info:
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Nlm Unique ID: 9107463 Medline TA: Fetal Diagn Ther Country: Switzerland |
Other Details:
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Languages: eng Pagination: 101-5 Citation Subset: IM |
Copyright Information:
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2010 S. Karger AG, Basel. |
Affiliation:
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Cardiac Center, Children's Hospital of Philadelphia, University of Pennsylvania, 19104, USA. |
Export Citation:
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| MeSH Terms | |
Descriptor/Qualifier:
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Adult Cardiomegaly / embryology, surgery, ultrasonography Cardiopulmonary Bypass Ebstein Anomaly / diagnosis*, surgery Female Fetal Diseases / ultrasonography Gestational Age Heart Atria / surgery, ultrasonography Humans Infant, Newborn Lung / embryology*, ultrasonography Magnetic Resonance Imaging Pregnancy Prenatal Diagnosis / methods* Pulmonary Artery / embryology*, surgery Tricuspid Valve / abnormalities*, embryology, surgery Tricuspid Valve Insufficiency / surgery, ultrasonography* Ultrasonography, Prenatal |
From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine
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