Document Detail


Tremor, ataxia and dementia in older men may indicate a carrier of the fragile X syndrome.
MedLine Citation:
PMID:  12791039     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Recently it has been reported that late-onset tremor, gait unsteadiness and dementia can be associated with brain atrophy in males of normal intelligence and the pre-mutation carrier state of the fragile X syndrome. We have shown, by means of a telephone survey, that this association is probably causal rather than coincidental. These findings have uncovered another testable cause of late-onset neurological symptoms in males, which also has serious genetic implications for their daughters who are at risk of having sons with full mutations causing mental handicap - the fragile X syndrome.
Authors:
C Rogers; M W Partington; G M Turner
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Publication Detail:
Type:  Journal Article    
Journal Detail:
Title:  Clinical genetics     Volume:  64     ISSN:  0009-9163     ISO Abbreviation:  Clin. Genet.     Publication Date:  2003 Jul 
Date Detail:
Created Date:  2003-06-06     Completed Date:  2004-02-18     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  0253664     Medline TA:  Clin Genet     Country:  Denmark    
Other Details:
Languages:  eng     Pagination:  54-6     Citation Subset:  IM    
Affiliation:
Hunter Genetics, The Hunter Area Health Service, Waratah, New South Wales, Australia.
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MeSH Terms
Descriptor/Qualifier:
Aged
Aged, 80 and over
Ataxia / genetics*
Dementia / genetics*
Fragile X Syndrome / genetics*
Heterozygote
Humans
Male
Middle Aged
Tremor / genetics*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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