Document Detail


Treatment with a farnesyltransferase inhibitor improves survival in mice with a Hutchinson-Gilford progeria syndrome mutation.
MedLine Citation:
PMID:  18082640     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Hutchinson-Gilford progeria syndrome (HGPS) is a progeroid syndrome characterized by multiple aging-like disease phenotypes. We recently reported that a protein farnesyltransferase inhibitor (FTI) improved several disease phenotypes in mice with a HGPS mutation (Lmna(HG/+)). Here, we investigated the impact of an FTI on the survival of Lmna(HG/+) mice. The FTI significantly improved the survival of both male and female Lmna(HG/+) mice. Treatment with the FTI also improved body weight curves and reduced the number of spontaneous rib fractures. This study provides further evidence for a beneficial effect of an FTI in HGPS.
Authors:
Shao H Yang; Xin Qiao; Loren G Fong; Stephen G Young
Publication Detail:
Type:  Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't     Date:  2007-11-26
Journal Detail:
Title:  Biochimica et biophysica acta     Volume:  1781     ISSN:  0006-3002     ISO Abbreviation:  Biochim. Biophys. Acta     Publication Date:    2008 Jan-Feb
Date Detail:
Created Date:  2008-02-11     Completed Date:  2008-04-04     Revised Date:  2011-01-10    
Medline Journal Info:
Nlm Unique ID:  0217513     Medline TA:  Biochim Biophys Acta     Country:  Netherlands    
Other Details:
Languages:  eng     Pagination:  36-9     Citation Subset:  IM    
Affiliation:
Department of Medicine/Division of Cardiology, David Geffen School of Medicine, University of California, Los Angeles, Los Angeles, CA, USA.
Export Citation:
APA/MLA Format     Download EndNote     Download BibTex
MeSH Terms
Descriptor/Qualifier:
Animals
Farnesyltranstransferase / antagonists & inhibitors*,  metabolism
Female
Lamin Type A / genetics,  metabolism
Male
Mice
Mice, Inbred C57BL
Mice, Transgenic
Mutation
Phenotype
Progeria / drug therapy*,  enzymology,  genetics*
Survival Rate
Grant Support
ID/Acronym/Agency:
AR050200/AR/NIAMS NIH HHS; HL76839/HL/NHLBI NIH HHS; HL86683/HL/NHLBI NIH HHS; R01 AR050200-01/AR/NIAMS NIH HHS; R01 AR050200-02/AR/NIAMS NIH HHS; R01 AR050200-02S1/AR/NIAMS NIH HHS; R01 AR050200-03/AR/NIAMS NIH HHS; R01 AR050200-04/AR/NIAMS NIH HHS; R01 AR050200-05/AR/NIAMS NIH HHS; R01 AR050200-06/AR/NIAMS NIH HHS; R01 HL076839-01A1/HL/NHLBI NIH HHS; R01 HL076839-02/HL/NHLBI NIH HHS; R01 HL076839-03/HL/NHLBI NIH HHS
Chemical
Reg. No./Substance:
0/Lamin Type A; EC 2.5.1.29/Farnesyltranstransferase
Comments/Corrections

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


Previous Document:  trans-Arachidonic acids induce a heme oxygenase-dependent vasorelaxation of cerebral microvasculatur...
Next Document:  A quantitative and morphometric study of tryptase-positive mast cells in cutaneous leprosy lesions.