Document Detail


Treatment of hyperacusis in Williams syndrome with bilateral conductive hearing loss.
MedLine Citation:
PMID:  11699823     Owner:  NLM     Status:  MEDLINE    
Abstract/OtherAbstract:
Williams syndrome (WS) is a rather rare congenital disorder characterised by a series of cardiovascular, maxillo-facial and skeletal abnormalities. It sometimes displays otorhinolaryngological symptoms because of the relatively high incidence of secretory otitis media and hyperacusis, which may be present in up to 95% of patients. The present paper describes a case of WS associated with bilateral conductive hearing loss which was not related to secretory otitis media. Hyperacusis was, moreover, present in spite of the conductive deafness. Surgical or prosthetic treatment of hearing loss was delayed because of hyperacusis. Treatment of the hyperacusis by acoustic training, instead, yielded excellent, long-lasting remission of the symptoms.
Authors:
C Miani; P Passon; A M Bracale; A Barotti; N Panzolli
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Publication Detail:
Type:  Case Reports; Journal Article    
Journal Detail:
Title:  European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery     Volume:  258     ISSN:  0937-4477     ISO Abbreviation:  Eur Arch Otorhinolaryngol     Publication Date:  2001 Sep 
Date Detail:
Created Date:  2001-11-08     Completed Date:  2002-02-26     Revised Date:  2004-11-17    
Medline Journal Info:
Nlm Unique ID:  9002937     Medline TA:  Eur Arch Otorhinolaryngol     Country:  Germany    
Other Details:
Languages:  eng     Pagination:  341-4     Citation Subset:  IM    
Affiliation:
Surgical Sciences Department, University of Udine School of Medicine, Italy. cmiani@dsc.uniud.it
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MeSH Terms
Descriptor/Qualifier:
Acoustic Stimulation / methods*
Adult
Audiometry, Pure-Tone / methods
Auditory Threshold / physiology
Female
Hearing Loss, Bilateral / complications*,  diagnosis,  therapy*
Hearing Loss, Conductive / complications*,  diagnosis,  therapy*
Humans
Hyperacusis / complications,  diagnosis,  therapy*
Severity of Illness Index
Tinnitus / complications
Williams Syndrome / complications*

From MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine


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